Management of Esophageal Lung in a Patient With VACTERL Anomalies

The American Surgeon
Kevin N HarrellCurtis S Koontz

Abstract

Esophageal lung is a rare type of bronchopulmonary foregut malformation where an anomalous main bronchus arises from the esophagus rather than the trachea. This differentiates from an esophageal bronchus where a lobar bronchus arises from the esophagus. Fewer than 30 of these anomalies have been reported in the literature. A female infant was born at 35 weeks gestational age and found to have multiple congenital abnormalities including cleft palate, long-gap esophageal atresia, tracheoesophageal fistula (TEF), imperforate anus, and renal anomalies. She initially underwent thoracoscopic ligation of TEF with colostomy and mucus fistula creation. Bronchoscopy found no right mainstem bronchus, and subsequent computed tomography scan was consistent with possible esophageal bronchus. Esophagoscopy through the gastrostomy discovered a fistulous connection between the distal esophagus and anomalous main right bronchus.Right thoracotomy with pneumonectomy of the hypoplastic lung was performed. She subsequently underwent vaginostomy for hydrometrocolpos. Her proximal esophagus was diverted with a cervical esophagostomy for control of secretions. She also required tracheotomy and is currently at home on minimal ventilator settings awaitin...Continue Reading

References

Aug 17, 2011·Journal of Pediatric Surgery·Nidhi SugandhiDevendra K Gupta
Jun 16, 2018·Radiology Case Reports·Ali AlsaadiAltaf Hussain Gora
Dec 24, 2018·American Journal of Medical Genetics. Part C, Seminars in Medical Genetics·Benjamin D Solomon

❮ Previous
Next ❯

Related Concepts

Related Feeds

Birth Defects

Birth defects encompass structural and functional alterations that occur during embryonic or fetal development and are present since birth. The cause may be genetic, environmental or unknown and can result in physical and/or mental impairment. Here is the latest research on birth defects.

Related Papers

Journal of Pediatric Surgery
Nidhi SugandhiDevendra K Gupta
Clinical Nuclear Medicine
J R Sty, M H Wolff
The Annals of Thoracic Surgery
Raghav MurthyNicholas Saenz
© 2021 Meta ULC. All rights reserved