Management of general anesthesia in a child with Miller-Dieker syndrome: a case report

JA Clinical Reports
Chiaki WakiguchiYuichi Kanmura

Abstract

Miller-Dieker syndrome (MDS) is a rare disorder characterized by type I lissencephaly and a distinctive facial appearance that may include prominent forehead, bitemporal hollowing, and micrognathia. MDS is associated with epilepsy. We here report an 18-month-old girl with MDS who required general anesthesia. The child had an extremely low Bispectral Index (BIS) value prior to undergoing general anesthesia. Her perioperative course was uneventful. This case highlights some of the important anesthetic concerns in patients with MDS, which include potentially difficult airways and extremely low BIS values.

References

Sep 3, 2003·Paediatric Anaesthesia·H Sahajananda, Jeevan Meneges
Apr 9, 2005·Epilepsia·Renzo Guerrini
Jan 24, 2006·Anesthesia and Analgesia·Senthilkumar SadhasivamMehernoor F Watcha
Apr 4, 2008·Paediatric Anaesthesia·Abraham J ValkenburgFrank Weber
Oct 27, 2010·International Journal of Pediatrics·Maria SammartinoAlessandro D'Addessi
May 2, 2013·Neurology. Clinical Practice·David T HsiehAnn-Christine Duhaime

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Citations

Apr 21, 2021·British Journal of Nursing : BJN·Amanda CarrNicola York

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Methods Mentioned

BETA
MDS
cesarean section
X-ray
sedation
circumcision

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