PMID: 9179809May 1, 1997Paper

Mayer-Rokitansky-Kuster-Hauser syndrome diagnosed by magnetic resonance imaging in a 15-year-old girl

Journal of Pediatric and Adolescent Gynecology
P D RussM A Koyle

Abstract

Mayer-Rokitansky-Kuster-Hauser syndrome diagnosed by magnetic resonance imaging (MRI) in a 15-year-old girl with primary amenorrhea is reported. The presentation, MRI, and the subsequent evaluation and treatment of an adolescent female patient with Rokitansky syndrome are described. Correlation is made with previous clinical, pathologic, and imaging reports in the literature. An adolescent girl with primary amenorrhea was referred to our institution for completion of her diagnostic work-up. Previous limited evaluations suggested the presence of anomalies of the genitourinary tract. Further delineation of the suspected congenital defects was necessary. The 15-year-old female patient was evaluated by the gynecology service. Diagnostic radiology and pediatric urology were consulted. MRI, physical examination under anesthesia, and cystoscopy were performed. After initial nonoperative treatment, the patient underwent hysterectomy and sigmoid vaginoplasty. The patient's primary amenorrhea was explained. Mayer-Rokitansky-Kuster-Hauser syndrome was diagnosed. Vaginal agenesis and widely separated rudimentary uterine horns were well shown by the MRI. Associated skeletal anomalies were noted. A treatment plan was initiated based on a goo...Continue Reading

References

Mar 1, 1987·Radiology·K TogashiM Ohshima

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Citations

Jun 29, 1999·Pediatric Clinics of North America·B Schroeder, J S Sanfilippo
Jun 12, 2002·Journal of Pediatric and Adolescent Gynecology·Katherine E EconomyMarc R Laufer
Jul 16, 2003·Radiographics : a Review Publication of the Radiological Society of North America, Inc·Sahar N Saleem
Aug 19, 2000·Seminars in Pediatric Surgery·A Stallion
Jun 6, 2009·Journal of Pediatric and Adolescent Gynecology·Huseyin OzkurtMuzaffer Basak
Sep 11, 1999·Obstetrical & Gynecological Survey·C L TemplemanS P Hertweck

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