Medical management update: Peutz Jeghers syndrome

Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontics
Paola HighamEric T Stoopler

Abstract

Peutz Jeghers syndrome (PJS) is an autosomal dominant disease characterized by hamartomatous polyposis and distinct mucocutaneous pigmentation. PJS is associated with an increased risk for several cancers and other complications such as small intestine intussusception, short bowel syndrome, and anemia. Medical management mainly consists of treatment of the polyps and surveillance. This medical management update will review clinical concepts, therapeutic advances, and emphasize features of PJS important to the oral health care provider.

References

Feb 12, 1976·The New England Journal of Medicine·J F Desforges
Dec 1, 1992·Archives of Dermatology·R G Geronemus
Nov 1, 1989·Gut·A D SpigelmanR K Phillips
Jun 11, 1987·The New England Journal of Medicine·F M GiardielloG D Luk
Aug 1, 1987·Digestive Diseases and Sciences·K WadaK Wada
Jul 15, 1986·American Journal of Ophthalmology·E I Traboulsi, I H Maumenee
Jul 1, 1980·Cancer·J M CantúA Hernández
Dec 1, 1993·Journal of the American Academy of Dermatology·N J LoweM Chalet
Nov 1, 1995·Journal of Oral Pathology & Medicine : Official Publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology·E A FieldW R Tyldesley
Dec 1, 1996·Journal of Medical Genetics·C BrassettE R Maher
Feb 25, 1998·Journal of Medical Genetics·S OlschwangI Tomlinson
Dec 5, 1998·American Journal of Human Genetics·H MehenniS E Antonarakis
Apr 27, 1999·Lancet·A M WestermanJ H Wilson
Jun 24, 1999·Cellular and Molecular Life Sciences : CMLS·A Hemminki
Jun 30, 2000·The New England Journal of Medicine·G SteinbachG Kelloff
Jun 30, 2000·Human Mutation·L A BoardmanS N Thibodeau
Dec 20, 2002·Gastroenterology Clinics of North America·Lisa A Boardman
Feb 13, 2003·Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontics·Scott S Derossi, Sree Raghavendra
Sep 26, 2003·Pediatric Radiology·Sebuh KurugogluUgur Korman
Oct 21, 2003·The Annals of Pharmacotherapy·Jill M Herendeen, Celeste Lindley
Feb 19, 2004·European Journal of Human Genetics : EJHG·Nathalie Le MeurThierry Frébourg
Jul 23, 2004·Journal of Pediatric Gastroenterology and Nutrition·R HindsJ M Fell
May 3, 2005·Journal of Medical Genetics·V SchumacherB Royer-Pokora
Nov 23, 2005·Anesthesia and Analgesia·Lawrence T GoodnoughRichard Spence
Dec 6, 2005·The Surgical Clinics of North America·Lena M Napolitano
Jun 8, 2006·Journal of the National Cancer Institute·Sabine GröschGerd Geisslinger
Sep 5, 2006·Cellular and Molecular Life Sciences : CMLS·T J McGarrity, C Amos
Dec 13, 2006·Clinical Gastroenterology and Hepatology : the Official Clinical Practice Journal of the American Gastroenterological Association·Billy BourkeTim Bohane
Feb 19, 2008·Clinical Cancer Research : an Official Journal of the American Association for Cancer Research·Chongjuan WeiMarsha L Frazier
Mar 26, 2008·Heart Failure Reviews·Garry J Handelman, Nathan W Levin
Apr 9, 2008·Nutrition in Clinical Practice : Official Publication of the American Society for Parenteral and Enteral Nutrition·Susan F Clark
Jul 9, 2008·Scandinavian Journal of Gastroenterology·Evangelos KalaitzakisIngvar Bosaeus
Aug 2, 2008·The Surgical Clinics of North America·Daniel Calva, James R Howe
Dec 3, 2008·European Journal of Gastroenterology & Hepatology·Herbert Tilg

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Citations

Nov 22, 2013·PloS One·Asadur TchekmedyianThomas McGarrity
Mar 19, 2016·Intractable & Rare Diseases Research·Ran WangXiaozhong Guo
Sep 17, 2013·Dental Clinics of North America·Faizan Alawi
Jan 16, 2013·Journal of the American Academy of Dermatology·Kejal R ShahAlan Menter
Feb 18, 2015·Oral Surgery, Oral Medicine, Oral Pathology and Oral Radiology·Darcy FernandesAndreia Bufalino
Jun 28, 2017·Tumour Biology : the Journal of the International Society for Oncodevelopmental Biology and Medicine·Hong-Yu ChenShou-Bin Ning
Feb 17, 2018·Head and Neck Pathology·Hattan ZakiAlfredo Aguirre
Oct 19, 2011·Journal of Gastrointestinal Surgery : Official Journal of the Society for Surgery of the Alimentary Tract·Hong WangXiu-Jie Wang
Aug 12, 2014·World Journal of Gastroenterology : WJG·Laura Valle
Feb 21, 2019·International Journal of Oral Science·En LuoQianming Chen
Sep 13, 2017·Middle East Journal of Digestive Diseases·Ran WangXiaozhong Guo

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