PMID: 7335098Oct 1, 1981Paper

Moyamoya like vascular disease in tuberous sclerosis (author's transl)

Monatsschrift Kinderheilkunde : Organ der Deutschen Gesellschaft für Kinderheilkunde
H H KramerH Seibert

Abstract

A 12 years and 8 months old girl with tuberous sclerosis developed focal motor and sensory seizures and hemiplegias initially right-sided and later left-sided. Cerebral angiography showed bilateral and symmetrical vascular network with teleangiectasias in the region of the basal ganglia and bilateral stenoses and ectasias of the middle cerebral artery. It is discussed whether this is a case of atypical Moyamoya disease or whether the bilateral basal networks are blood vessel dysplasias and part of the neurocutaneous phakomatosis.

Related Concepts

Related Feeds

Basal Ganglia

Basal Ganglia are a group of subcortical nuclei in the brain associated with control of voluntary motor movements, procedural and habit learning, emotion, and cognition. Here is the latest research.