MR imaging of arrhythmogenic right ventricular dysplasia: What the radiologist needs to know

Diagnostic and Interventional Imaging
A TavanoA Jacquier

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is an inherited heart muscle disease that predominantly affects the right ventricle. Clinical manifestations are related to severe ventricular arrhythmia that may lead to sudden death, mostly in young patients. Magnetic resonance imaging (MRI), included in the new diagnostic criteria since 2010, aims to detect segmental and global wall motion abnormalities, reduced ejection fraction, right ventricular dilatation and right ventricular diastolic/systolic dysfunction. An MRI assessment of the right ventricle is often challenging, partly because the MRI diagnostic criteria have some limitations, and also because it requires a significant learning curve due to the low prevalence of the disease. Therefore, this article aims to review the pathophysiology of the disease, the cardiac MRI protocol, images of the various stages of this affection as well as the differential diagnosis.

References

Jun 2, 2004·Journal of Magnetic Resonance Imaging : JMRI·Harikrishna TandriDavid A Bluemke
Nov 8, 2005·Journal of Computer Assisted Tomography·Jan FritzDavid A Bluemke
Jun 24, 2008·Journal of Cardiovascular Magnetic Resonance : Official Journal of the Society for Cardiovascular Magnetic Resonance·Aditya JainDavid A Bluemke
Sep 9, 2010·European Heart Journal·Philippe CharronUNKNOWN European Society of Cardiology Working Group on Myocardial and Pericardial Diseases
Oct 10, 2013·Journal of Cardiovascular Magnetic Resonance : Official Journal of the Society for Cardiovascular Magnetic Resonance·Christopher M KramerUNKNOWN Society for Cardiovascular Magnetic Resonance Board of Trustees Task Force on Standardized Protocols

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Citations

Aug 30, 2019·Korean Journal of Radiology : Official Journal of the Korean Radiological Society·Yeseul JoHwan Seok Yong
Feb 8, 2020·Cardiology in Review·Amer SayedJason T Jacobson

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