Multifocal distribution of pulmonary capillary haemangiomatosis

Histopathology
A Erbersdobler, A Niendorf

Abstract

We investigated a case of pulmonary capillary haemangiomatosis, a rare condition, to determine the extent of the pathological changes within the lungs. Systematic histological sampling has not previously been performed in this condition. A 52-year-old woman with a history of ischaemic cardiomyopathy suffered from repeated respiratory infections, which were attributed to chronic pulmonary congestion. She died suddenly of fulminant pulmonary thromboembolism. An autopsy was performed and lung tissue was sampled at multiple sites. Beside passive congestion, the lungs showed well-circumscribed areas containing proliferations of small capillaries infiltrating the pulmonary septa and the walls of otherwise normal blood vessels and bronchi. The most severely affected areas were found to be in the periphery of both lower lobes. A diagnosis of pulmonary capillary haemangiomatosis was made. This is the first case of pulmonary capillary haemangiomatosis in which systematic histological sampling has been performed. Mapping of lesions disclosed the multifocal distribution of pulmonary capillary haemangiomatosis in this patient.

References

Nov 1, 1978·Histopathology·C A WagenvoortJ Spijker
Jan 1, 1992·Respiration; International Review of Thoracic Diseases·C DomingoJ Morera
Sep 1, 1989·The American Review of Respiratory Disease·C N FaberI L Paradis
Feb 1, 1989·Histopathology·S S WagenaarJ M van den Bosch
Nov 1, 1986·Human Pathology·V TronA Churg
Jul 1, 1985·British Journal of Diseases of the Chest·D Heath, R Reid
Jan 1, 1974·Virchows Archiv. A, Pathological Anatomy and Histology·C A Wagenvoort, N Wagenvoort
Sep 1, 1996·Histopathology·H IshiiH Koshino

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Citations

Feb 17, 2005·Pediatric Radiology·Cicero J T A SilvaSimone A Mandelstam
Jul 5, 2006·The American Journal of Surgical Pathology·Sylvie LantuéjoulAndrew G Nicholson
Nov 19, 2011·Histopathology·Susumu Matsukuma, Kimiya Sato
Mar 1, 2005·Forensic Science International : Synergy·Michael Tsokos, Andreas Erbersdobler
Aug 11, 2004·Cardiology Clinics·Eunhee S Yi
Jun 15, 2004·Journal of the American College of Cardiology·Giuseppe G PietraR M Tuder
Feb 9, 2017·The New England Journal of Medicine·T Bernard KinaneEugene J Mark
May 29, 2020·European Respiratory Review : an Official Journal of the European Respiratory Society·Jason WeatheraldDavid Montani

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