Nasopharyngeal encephalocele: report of transcranial and transpalatal repair with a 25-year follow-up

The Journal of Craniofacial Surgery
Malcolm A LesavoyBrian P Dickinson

Abstract

: Encephaloceles are an extension or protrusion of any intracranial matter through a cranial bone defect. The sphenoethmoidal encephalocele is often fatal. For those who survive long enough, expeditious repair is critical. We report a case that was repaired successfully via a combined transcranial and transpalatal approach, and because of successful repair, the patient underwent multiple secondary reconstructions resulting in a 25-year follow-up. : A 3960-g, term male infant from a normal gestation was delivered via cesarean delivery for breech position. Initial examination revealed a 2 x 3-cm gray intraoral nasopharyngeal mass with smooth mucosal covering extruding through a midline palatal cleft. At 4 weeks of life, extradural and intradural exploration of the encephalocele was performed via a bifrontal craniotomy. At 15 months of age, the patient underwent median cleft lip repair. At 6 years of age, hypertelorism was corrected by wedge resection of the frontal and nasal bones and medial mobilization of the orbits. Follow-up was continued until 25 years of age, which revealed excellent maintenance of correction. : Sphenoethmoidal encephalocele is a rare sporadic congenital cranial floor defect associated with typical facial a...Continue Reading

References

Sep 1, 1985·The Annals of Otology, Rhinology, and Laryngology·M A Kenna
Nov 1, 1965·Archives of Otolaryngology·R Blumenfeld, E M Skolnik
Jun 1, 1993·Archives of Disease in Childhood·H M Fortnum, A C Davis

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Citations

May 2, 2015·Journal of Korean Neurosurgical Society·Alexander HammerHans-Herbert Steiner

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