Noncompaction of the left ventricle: a new cardiomyopathy is presented to the clinician

São Paulo Medical Journal = Revista Paulista De Medicina
Fábio Cañellas MoreiraFernando Lucchese

Abstract

Noncompaction of the left ventricular myocardium is a morphogenetic abnormality involving loss of compaction of the myocardial fiber meshwork during intrauterine life. It is an extremely rare condition, accounting for only 0.05% of the cases evaluated in databanks. It has been described in both genders, in many ethnic groups and at different ages. Recently published studies of case series have shown a high mortality rate among these patients during follow-up of up to 48 months. Many cases have so far been misdiagnosed due to poor knowledge of the findings relating to this syndrome. There needs to be an attempt at early and accurate diagnosis, because of the need to investigate the patients family upon such diagnosis, and today this can be achieved using echocardiographic criteria.

References

Oct 23, 1997·American Journal of Human Genetics·S B BleylK Ward
Aug 22, 2000·Arquivos brasileiros de cardiologia·J EliasC A Peixoto
Oct 16, 2001·The International Journal of Cardiovascular Imaging·Y HamamichiT Kamiya
Feb 19, 2002·Laboratory Investigation; a Journal of Technical Methods and Pathology·Eduardo ZambranoPei Hui
Dec 5, 2002·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Süheyla OzkutluHuda Elshershari
Mar 6, 2003·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·R Ian WilliamsAlan G Fraser
Jan 9, 2004·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Sulafa Khalid M AliMichael J Godman
Jan 9, 2004·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Claudia Stöllberger, Josef Finsterer
Jan 12, 2005·European Journal of Heart Failure·Ming Lee LinDavid Prior

❮ Previous
Next ❯

Citations

Jan 19, 2016·Revista Portuguesa De Cardiologia : Orgão Oficial Da Sociedade Portuguesa De Cardiologia = Portuguese Journal of Cardiology : an Official Journal of the Portuguese Society of Cardiology·Mariana MagalhãesJosé Carlos Areias
Oct 7, 2008·Journal of Cardiothoracic and Vascular Anesthesia·Gregory W FischerJill Kalman
Mar 23, 2012·Korean Journal of Radiology : Official Journal of the Korean Radiological Society·Heon LeeU Joseph Schoepf
Mar 11, 2010·Journal of Thoracic Imaging·Navid A ZenoozRobert C Gilkeson

❮ Previous
Next ❯

Related Concepts

Related Feeds

Cardiomyopathy

Cardiomyopathy is a disease of the heart muscle, that can lead to muscular or electrical dysfunction of the heart. It is often an irreversible disease that is associated with a poor prognosis. There are different causes and classifications of cardiomyopathies. Here are the latest discoveries pertaining to this disease.