PMID: 6969676Jan 1, 1981Paper

Obstructive jaundice in children with histiocytosis X

Gastroenterology
A LeblancD Alagille

Abstract

Prolonged cholestasis was observed in 6 children with histiocytosis X. Operative cholangiograms confirmed the patency of the extrahepatic biliary tree and showed marked distortion of intrahepatic bile ducts resembling that observed in sclerosing cholangitis. Histologic examination showed portal fibrosis in all patients; only one was found to have portal histiocytic infiltration. The subsequent course confirmed the ominous significance of cholestasis in histiocytosis X, a rare finding in this disease: One patient died of progressive liver failure and three others from sepsis after unsuccessful attempts to improve the condition of the liver with chemotherapy.

Citations

Jan 1, 1995·Critical Reviews in Oncology/hematology·R M Egeler, M E Nesbit
Nov 20, 1997·Clinical Radiology·Y L ChanC Y Lee
Oct 3, 1999·European Journal of Cancer : Official Journal for European Organization for Research and Treatment of Cancer (EORTC) [and] European Association for Cancer Research (EACR)·R J Arceci
May 1, 1984·Gut·H H ThompsonW P Longmire
May 10, 2011·Clinics and Research in Hepatology and Gastroenterology·Meya AbdallahJean Cabane
May 12, 2009·Archives de pédiatrie : organe officiel de la Sociéte française de pédiatrie·E Georget-BouquinetJ Donadieu
Apr 1, 1984·Gastrointestinal Endoscopy·S C Hauser, T E Bynum
Apr 14, 2010·Acta Ophthalmologica·Kristina Teär FahnehjelmAntal Nemeth
Jan 1, 1987·The American Journal of Medicine·F J RamosA López-Borrasca
Feb 1, 1996·Pediatric Clinics of North America·C F McEvoy, F J Suchy
Aug 9, 2001·Best Practice & Research. Clinical Gastroenterology·G Mieli-Vergani, D Vergani
Jun 8, 2006·Current Surgery·Manuel CaceresMichael Boyle
Jan 1, 1994·The Journal of Pediatrics·D DebrayO Bernard

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