Office-Based Anesthetic and Oral Surgical Management of a Child With Hereditary Sensory Autonomic Neuropathy Type IV: A Case Report

Anesthesia Progress
Shamit PrabhuUday N Reebye

Abstract

Hereditary sensory and autonomic neuropathy type IV (HSAN IV), or congenital insensitivity to pain with anhidrosis, is an exceptionally rare genetic disorder that results in the complete loss of pain and temperature sensation as well as anhidrosis. Anesthetic management of these patients can be difficult because of significantly increased risks during general anesthesia. Literature on perioperative anesthetic management is typically written in the context of a hospital setting. As such, our case presents a unique report on the anesthetic management of a HSAN IV patient who presented for extraction of 2 teeth in an office-based setting. In determining how to safely manage the procedure, we decided against general anesthesia as we lacked the facilities and equipment to safely handle previously reported complications. We were successful in providing sedation with nitrous oxide in oxygen and applying 20% benzocaine topical ointment on the surgical site in lieu of administering general anesthesia. We had an anesthesiologist present and obtained intravenous access prior to the surgery to help manage any complications. This report provides support that simple dental extractions can be accomplished safely in the HSAN IV patient in the ...Continue Reading

References

Aug 1, 1994·Brain : a Journal of Neurology·P K ThomasN H Wadia
Nov 3, 1998·Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontics·A AmanoI Morisaki
Mar 24, 1999·American Journal of Ophthalmology·R YagevT Lifshitz
Aug 30, 2000·Clinical Neurophysiology : Official Journal of the International Federation of Clinical Neurophysiology·M NolanoG Caruso
Jun 18, 2003·International Archives of Allergy and Immunology·S BoniniL Aloe
Dec 8, 2005·European Journal of Human Genetics : EJHG·Ahmed BouhoucheMohamed Yahyaoui
Dec 20, 2005·Oral Surgery, Oral Medicine, Oral Pathology, Oral Radiology, and Endodontics·Jonathan ButlerDavid Webb
Jun 16, 2006·Neuromolecular Medicine·Michaela Auer-GrumbachThomas R Pieber
Dec 15, 2006·Nature·James J CoxC Geoffrey Woods
Aug 5, 2009·Brain : a Journal of Neurology·Annelies RotthierVincent Timmerman
Sep 17, 2009·Dental Traumatology : Official Publication of International Association for Dental Traumatology·Beatriz Gonçalves NevesGloria Fernanda Castro
Oct 6, 2010·American Journal of Human Genetics·Annelies RotthierVincent Timmerman
May 3, 2011·Nature Genetics·Christopher J KleinPeter J Dyck
Jan 25, 2012·Nature Reviews. Neurology·Annelies RotthierKatrien Janssens
Apr 24, 2012·Annals of Neurology·Simon EdvardsonOrly Elpeleg
Feb 1, 2013·Neurology·Christopher J KleinGarth A Nicholson
Sep 17, 2013·Nature Genetics·Enrico LeipoldIngo Kurth
Nov 26, 2014·Pediatrics International : Official Journal of the Japan Pediatric Society·Nobuhiko HagaUNKNOWN Japanese Research Group on Congenital Insensitivity to Pain
May 26, 2015·Nature Genetics·Ya-Chun ChenJan Senderek
Jul 1, 2015·International Journal of Clinical Pediatric Dentistry·K S RavichandraDisha Lakhotia
Sep 18, 2015·European Journal of Human Genetics : EJHG·Christopher Geoffrey WoodsIngo Kurth
Mar 16, 2016·Journal of Medical Genetics·Stella ZhangGeoffrey Woods
Sep 18, 2016·European Journal of Paediatric Neurology : EJPN : Official Journal of the European Paediatric Neurology Society·Babar KayaniDeborah M Eastwood

❮ Previous
Next ❯

Related Concepts

Related Feeds

Birth Defects

Birth defects encompass structural and functional alterations that occur during embryonic or fetal development and are present since birth. The cause may be genetic, environmental or unknown and can result in physical and/or mental impairment. Here is the latest research on birth defects.

Related Papers

Journal of Clinical and Diagnostic Research : JCDR
Neena Indavara EregowdaRoopa Korishettar Basavraj
Revista brasileira de anestesiologia
Carlos Rogério Degrandi OliveiraFelipe Souza Thyrso de Lara
Journal of the Royal Society of Medicine
A E HaworthJ Walker
© 2022 Meta ULC. All rights reserved