Old syndrome-new approach: Mauriac syndrome treated with continuous insulin delivery

SAGE Open Medical Case Reports
Mirjana Kocova, Liljana Milenkova

Abstract

Mauriac syndrome has rarely been reported in children and adolescents with a poorly controlled diabetes mellitus type 1. However, it still occurs despite the worldwide improvements of metabolic control. The risks have not been elucidated. We present a 13.5-year-old boy with a typical clinical presentation of Mauriac syndrome consisting of growth delay, cushingoid appearance, hepatomegaly, and delayed puberty. A stepwise correction of glycemic control was introduced using continuous insulin delivery. All symptoms improved during the 2.5-year follow-up. No retinopathy occurred. This patient with Mauriac syndrome followed with continuous glucose monitoring and treated with continuous insulin delivery, resulting in no retinopathy after 2.5 years of follow-up. We suggest that this approach should be recommended in patients with Mauriac syndrome.

References

Sep 1, 1984·European Journal of Pediatrics·H S Traisman, E S Traisman
Oct 19, 2000·Journal of Paediatrics and Child Health·C F MunnsJ Batch
Nov 2, 2001·Diabetes Research and Clinical Practice·A FranzeseG Valerio
Mar 16, 2007·Endocrine Practice : Official Journal of the American College of Endocrinology and the American Association of Clinical Endocrinologists·Shefali MaheshJose Bernardo Q Quintos
Dec 25, 2012·Diabetes Care·Komal Eram ImtiazFiona Karlson
Nov 20, 2013·Indian Journal of Endocrinology and Metabolism·Manish GutchKeshav Kumar Gupta
Jan 15, 2014·Archives of Disease in Childhood·E FitzpatrickN Hadzic

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Citations

Jan 9, 2019·Italian Journal of Pediatrics·Fortunato LombardoGiuseppina Salzano
Jan 21, 2021·Wiener medizinische Wochenschrift·Jan de LaffolieKlaus-Peter Zimmer
Apr 20, 2021·Clinical Pediatric Endocrinology : Case Reports and Clinical Investigations : Official Journal of the Japanese Society for Pediatric Endocrinology·Nor Azizah AbuNoor Shafina Mohd Nor

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