PMID: 9450825Feb 5, 1998Paper

Otologic and laryngologic manifestations of mucopolysaccharidoses after bone marrow transplantation

Otolaryngology--head and Neck Surgery : Official Journal of American Academy of Otolaryngology-Head and Neck Surgery
B PapsinS E Leighton

Abstract

Children with mucopolysaccharidosis have significant functional impairment of a number of systems because of deposition of glycosaminoglycans. The otolaryngologic system is affected, resulting in conductive and sensorineural hearing loss and voice abnormality. Eleven children who had undergone bone marrow transplantation had their hearing and voices assessed. Unmatched data from patients who had not undergone transplantation were collected for nonstatistical comparison. The hearing loss in children who had undergone bone marrow transplantation was variable but on average was less severe than in the younger children who had not undergone transplantation. The incidence of otitis media with effusion was diminished in the transplanted group. Approximately half had normal voices. Diminution of the progression of hearing loss and voice abnormality probably occurs in patients after treatment by bone marrow transplantation.

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Citations

Jan 23, 2008·Der Orthopäde·B LinkA Meurer
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Jan 24, 2008·Audiology & Neuro-otology·Yang-Sun ChoDong-Kyu Jin
Nov 26, 2009·International Journal of Pediatric Otorhinolaryngology·Stephen M WoldVirginia Proud
Jun 25, 2020·Journal of Inherited Metabolic Disease·Brigitte T A van den BroekPeter M van Hasselt
May 31, 2019·Orphanet Journal of Rare Diseases·Mehmet Umut AkyolUNKNOWN MPS Consensus Programme Co-Chairs
Aug 12, 2021·International Archives of Otorhinolaryngology·Cibele Gomes BicalhoAngelina Xavier Acosta

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