Abstract
Outcomes after right ventricle (RV) decompression in infants with pulmonary atresia with intact ventricular septum vary widely. Descriptions of outcomes are limited to small single-center studies. Neonates undergoing RV decompression for pulmonary atresia with intact ventricular septum were included from 4 pediatric centers. Primary end point was reintervention post-RV decompression; secondary end points included circulation type at latest follow-up. Ninety-nine patients (71 with pulmonary atresia with intact ventricular septum and 28 with virtual atresia) underwent RV decompression at median 3 (25th-75th, 2-5) days of age. Seventy-one patients (72%) underwent at least 1 reintervention after decompression. Median duration of follow-up was 3 years (range, 1-10). Freedom from reintervention was 51% at 1 month and 23% at 3 years. In multivariable analysis, reintervention was associated with virtual atresia (hazard ratio [HR], 0.51; 95% confidence interval [CI], 0.28-091;P=0.027), smaller RV length (HR, 0.94; 95% CI, 0.89-0.99;P=0.027), and ≤mild tricuspid regurgitation (TR; HR, 3.58; 95% CI, 2.04-6.30;P<0.001). Patients undergoing surgical shunt or ductal stent were less likely to have virtual atresia (HR, 0.36; 95% CI, 0.15-0.85;...Continue Reading
References
Nov 1, 1993·Circulation·T M GigliaJ E Lock
Apr 1, 1997·Catheterization and Cardiovascular Diagnosis·R N JustoL N Benson
Jun 1, 2000·The American Journal of Cardiology·L L MinichJ A Hawkins
Nov 22, 2002·Lancet·Gerald TulzerHelena M Gardiner
Jul 2, 2003·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·William A ZoghbiUNKNOWN American Society of Echocardiography
Jul 30, 2003·Circulation·Tilman HumplLee N Benson
Mar 31, 2004·The Journal of Thoracic and Cardiovascular Surgery·David A AshburnUNKNOWN Congenital Heart Surgeons Study members
May 30, 2006·The Annals of Thoracic Surgery·Kristine J GuleserianJohn E Mayer
Nov 14, 2006·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Renuka E PetersonStacey Drant
Feb 24, 2007·The American Journal of Cardiology·Kevin S RomanEdgar T Jaeggi
Mar 29, 2008·Journal of the American College of Cardiology·Helena M GardinerRodney C Franklin
Apr 15, 2008·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Michael D PettersenRichard A Humes
Jun 24, 2008·Ultrasound in Obstetrics & Gynecology : the Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology·R IacobelliS P Sanders
Aug 27, 2009·Pediatrics·Wayne TworetzkyAudrey C Marshall
Dec 5, 2009·European Journal of Echocardiography : the Journal of the Working Group on Echocardiography of the European Society of Cardiology·Abdenasser DrighilFadl AlFadly
May 11, 2010·Journal of the American Society of Echocardiography : Official Publication of the American Society of Echocardiography·Leo LopezTal Geva
Oct 19, 2012·Catheterization and Cardiovascular Interventions : Official Journal of the Society for Cardiac Angiography & Interventions·Babar Sultan HasanFrank A Pigula
Jun 20, 2013·Pediatric Cardiology·Matthew C SchwartzMatthew J Gillespie
Aug 26, 2014·The Annals of Thoracic Surgery·Adriaan W SchneiderMark G Hazekamp
Jul 25, 2015·Journal of the American College of Cardiology·Anita J Moon-GradyUNKNOWN International Fetal Cardiac Intervention Registry
Feb 18, 2016·Current Opinion in Pediatrics·Lindsay R Freud, Wayne Tworetzky
Citations
Sep 22, 2018·Congenital Heart Disease·Shiraz A MaskatiaRitu Sachdeva
Oct 19, 2017·Circulation·Andrew C GlatzAthar M Qureshi
Jun 19, 2018·Cardiology in the Young·Christopher J PetitBryan H Goldstein
Dec 10, 2019·Catheterization and Cardiovascular Interventions : Official Journal of the Society for Cardiac Angiography & Interventions·Holly Bauser-HeatonChristopher J Petit
Jun 12, 2019·Congenital Heart Disease·Christopher J PetitBryan H Goldstein
Apr 19, 2019·Circulation. Cardiovascular Interventions·Bryan H GoldsteinAndrew C Glatz
May 6, 2020·Pediatric Cardiology·Bassel Mohammad NijresJoseph J Vettukattil
Feb 23, 2019·Catheterization and Cardiovascular Interventions : Official Journal of the Society for Cardiac Angiography & Interventions·Athar M QureshiChristopher J Petit
Dec 20, 2019·Journal of the American Heart Association·George T NicholsonBryan H Goldstein
Aug 8, 2020·Echocardiography·Tamer YoldaşDilek Dilli
Jan 5, 2021·Pediatric Cardiology·Bryan H GoldsteinAndrew C Glatz
Mar 18, 2021·Cardiology in the Young·Joelle A PettusUNKNOWN Congenital Cardiac Research Collaborative
Oct 15, 2020·Cardiology in the Young·George T NicholsonChristopher J Petit
Sep 16, 2021·Pediatric Cardiology·Holly Bauser-HeatonChristopher J Petit
Sep 25, 2021·Pediatric Cardiology·Jun MuneuchiYoshie Ochiai
Apr 18, 2021·The Annals of Thoracic Surgery·Yuichiro SugitaniYoshie Ochiai