Paroxysmal episodes, "re-build up" phenomenon and moyamoya disease

Epileptic Disorders : International Epilepsy Journal with Videotape
Nomazulu DlaminiElaine Hughes

Abstract

Moyamoya disease is an idiopathic cerebral vasculopathy, which may be progressive or non-progressive. Non-idiopathic forms with an associated disease are called moyamoya-like syndrome. The electroencephalographic finding characteristically seen after hyperventilation in about 50% of children with cerebrovascular disease includes gradual frequency decrease and activation of amplitude of slow waves which appear after the disappearance or attenuation of ordinary build up. This is termed the "re-build up" phenomenon, which is rarely seen and therefore may be under-recognized. We present video telemetry during a transient ischaemic event of a child subsequently diagnosed with moyamoya-like syndrome. We highlight the potential for misdiagnosis of organic non-epileptic events. Hyperventilation during EEG should be avoided in children with known moyamoya disease.

Citations

Nov 25, 2014·Indian Journal of Pediatrics·Andrea AndradeMahendranath Moharir
Sep 19, 2019·Journal of Clinical Neuroscience : Official Journal of the Neurosurgical Society of Australasia·Jie BaiYong-Hong Liu
Mar 28, 2021·Pediatric Neurology·Anna L HuguenardJennifer M Strahle
Jan 29, 2021·Case Reports in Neurology·Shinichiro UchiyamaTakakazu Kawamata

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