Percutaneous interventional radiology procedures in patients with epidermolysis bullosa: modifications and challenges

AJR. American Journal of Roentgenology
Ertugrul MaviliBairbre Connolly

Abstract

The purpose of this study is to describe the role of interventional radiology in palliation and maintenance of nutritional support in children with epidermolysis bullosa, with a focus on safety and required procedural modifications. This was a retrospective study of all patients diagnosed with epidermolysis bullosa who underwent interventional radiology procedures between January 1991 and December 2008 at a pediatric tertiary care institution. The type of epidermolysis bullosa, the patient's age, the indication and type of interventional radiology procedure, modifications used, and complications were recorded. Fifteen patients (9 boys and 6 girls) with a diagnosis of epidermolysis bullosa underwent a total of 87 procedures during 82 different patient interventional radiology visits. Twenty-seven esophageal dilatations for symptoms of dysphagia, 11 percutaneous gastrostomy tube placements resulting from failure to thrive, 30 maintenance procedures, 15 central venous access device insertions, and three other procedures (nasojejunal tube insertion, liver biopsy, and inferior vena cava filter insertion) were performed. Modifications were related to anesthetic management, access, tissue handling, and dressings. Complications were ca...Continue Reading

References

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Nov 22, 2008·Journal of the American Academy of Dermatology·Warren R Heymann

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Citations

Jun 27, 2012·AJR. American Journal of Roentgenology·Stavros SpiliopoulosAndreas Adam

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