Perioperative Hemostatic Management in Ehlers-Danlos Syndrome: A Report of 2 Cases and Literature Review

Journal of Pediatric Hematology/oncology
Holly LindsayLakshmi V Srivaths

Abstract

Ehlers-Danlos syndrome (EDS) is associated with easy bruising and bleeding complications in the majority. Although bleeding complications are frequently observed during surgery in these patients, the perioperative hemostatic prophylaxis of patients with EDS is not standardized. We present 2 cases of effective perioperative hemostatic management of patients with EDS and review the literature to raise awareness of hemostatic issues during surgery and discuss medical options to consider for perioperative hemostatic management based on our clinical experience and literature review.

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Citations

Aug 5, 2016·Orphanet Journal of Rare Diseases·Albert BuschRené Wildenauer
Jul 23, 2019·Haemophilia : the Official Journal of the World Federation of Hemophilia·Rohith JesudasChristina M Laukaitis

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