PMID: 11924535Apr 2, 2002Paper

Plastic bronchitis in children with Fontan palliation: analogue to protein losing enteropathy?

Pediatric Cardiology
B StillerF K H van Landeghem

Abstract

We studied a 6-year-old boy and a 2-year-old girl with bronchitis fibroplastica following Fontan operation. Large endobronchial casts of rubber-like consistency resulted in life-threatening pulmonary failure. In one patient symptoms improved after optimizing heart function with diuretics, and in the other a dramatic improvement with the resolution of the clinical symptoms and normalized serum albumin followed subcutaneous high-molecular-weight heparin treatment. The severe relapse after discontinuation of the heparin medication and the once more successful treatment with heparin suggest that in addition to optimizing heart function, high-molecular-weight heparin might be a therapeutic option for this poorly understood condition.

References

Oct 1, 1990·Pediatric Cardiology·V ColloridiE Giglioni
Jan 1, 1987·The Annals of Otology, Rhinology, and Laryngology·J Werkhaven, L D Holinger
Feb 1, 1985·AJR. American Journal of Roentgenology·A BowenK S Oh
Jan 1, 1997·American Journal of Respiratory and Critical Care Medicine·M SeearE Cutz
May 30, 1998·The Journal of Thoracic and Cardiovascular Surgery·L MertensM Gewillig
Nov 2, 1999·Archives de pédiatrie : organe officiel de la Sociéte française de pédiatrie·F CounilM Voisin

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Citations

Sep 1, 2005·Pediatric Cardiology·J WilsonL Benson
May 5, 2010·The Journal of Laryngology and Otology·E HoskisonA Dux
Jul 1, 2010·Cardiology in the Young·Vanessa A GuimarãesEdmar Atik
Oct 29, 2003·Journal of Pediatric Gastroenterology and Nutrition·Brigitte Stiller
Jan 8, 2005·Pediatric Critical Care Medicine : a Journal of the Society of Critical Care Medicine and the World Federation of Pediatric Intensive and Critical Care Societies·Martin K WakehamJaveed Akhter
May 13, 2009·Pediatric Critical Care Medicine : a Journal of the Society of Critical Care Medicine and the World Federation of Pediatric Intensive and Critical Care Societies·Martin ZahorecPavol Kunovsky
Jun 16, 2010·International Journal of Pediatric Otorhinolaryngology·Diego PreciadoSukgi Choi
Jun 21, 2007·Transplantation Proceedings·J WongP B S Lai
Apr 1, 2008·Congenital Heart Disease·Gil WernovskyMarie M Gleason
May 21, 2013·Pharmacotherapy·Kristina BrooksKathleen A Stringer
May 30, 2006·The Annals of Thoracic Surgery·S Salman A ShahKarla G Christian
Jul 28, 2009·The Annals of Thoracic Surgery·Eric R GriffithsPedro del Nido
Sep 23, 2008·Anesthesia and Analgesia·Susan VergheseDiago Preciado
Mar 21, 2017·ASAIO Journal : a Peer-reviewed Journal of the American Society for Artificial Internal Organs·Po-Lin HsuJoseph B Zwischenberger

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