Positive Outcomes and Surgical Strategies for Bilateral Cochlear Implantation in a Child With X-Linked Deafness

The Annals of Otology, Rhinology, and Laryngology
Leslie KimEdward Eugene Dodson

Abstract

To recognize that bilateral cochlear implantation (CI) in X-linked deafness is safe, describe techniques to maximize successful electrode placement and minimize surgical risks, and recognize that normalization of hearing as well as language acquisition is achievable. A 6-month-old male patient presented with bilateral profound sensorineural hearing loss and was confirmed to have X-linked deafness secondary to POU3F4 gene mutation. Due to lack of benefit from amplification, he underwent bilateral CI in a staged fashion at 12 (right) and 15 months (left) of age. A transmastoid-facial recess approach was used bilaterally utilizing perimodiolar electrodes. High-flow gushers were controlled with muscle plugs. C-arm fluoroscopy was used during insertion of electrodes. Follow-up data are available for 12 months. No complications were encountered, including no postoperative cerebrospinal fluid (CSF) leakage or facial stimulation. Postoperative audiograms in aided conditions showed hearing thresholds <40 dB. At 11 months following activation of his second CI, he scored in the normal range for his chronological age on standardized language measures. With careful preparation and the assistance of intraoperative fluoroscopy, CI in patients...Continue Reading

References

Nov 17, 2007·Clinical Genetics·M B PetersenP J Willems
Feb 29, 2008·European Archives of Oto-rhino-laryngology : Official Journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : Affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery·Armagan IncesuluCem Kecik
Jan 22, 2011·The Annals of Otology, Rhinology, and Laryngology·Konstantina M StankovicLeila A Mankarious
May 21, 2011·AJNR. American Journal of Neuroradiology·B Y HuangM Castillo
Mar 9, 2013·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Woo Seok KangKwang-Sun Lee
Apr 5, 2012·The Laryngoscope·Selena E Heman-AckahJ Thomas Roland
Jan 11, 2014·European Archives of Oto-rhino-laryngology : Official Journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : Affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery·Jesper BilleTherese Ovesen
Mar 13, 2014·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Jin Woong ChoiByung Yoon Choi

❮ Previous
Next ❯

Citations

May 5, 2016·Cochlear Implants International·Haroon SaeedShakeel R Saeed
Jul 1, 2020·Otolaryngology--head and Neck Surgery : Official Journal of American Academy of Otolaryngology-Head and Neck Surgery·Joshua D SmithMarc C Thorne

❮ Previous
Next ❯

Methods Mentioned

BETA
cochlear implants
cochlear implant

Related Concepts

Related Feeds

Auditory Perception

Auditory perception is the ability to receive and interpret information attained by the ears. Here is the latest research on factors and underlying mechanisms that influence auditory perception.

CSF & Lymphatic System

This feed focuses on Cerebral Spinal Fluid (CSF) and the lymphatic system. Discover the latest papers using imaging techniques to track CSF outflow into the lymphatic system in animal models.

Related Papers

JAMA : the Journal of the American Medical Association
John K NiparkoCDaCI Investigative Team
Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
Isaac D ErbeleArnaldo Rivera
The Journal of Laryngology and Otology
Andrea BacciuS Bacciu
American Journal of Otolaryngology
Bridget HathawayBarton Branstetter
© 2021 Meta ULC. All rights reserved