Protein-losing enteropathy after Fontan operation for tricuspid atresia (imperforate tricuspid valve)

The Thoracic and Cardiovascular Surgeon
G CrupiL Parenzan

Abstract

Protein-losing enteropathy occurred in a 7-year-old girl with tricuspid atresia, concordant ventriculo-arterial connexions and a relatively large hypoplastic right ventricle, one year after an atrio-ventricular type of Fontan operation by means of a valveless woven Dacron conduit. Severe conduit regurgitation and a marked enlargement of the hypoplastic right ventricle were demonstrated at recatheterization. Insertion of a bioprosthetic valve at the base of the right atrial appendage led to a dramatic clinical recovery of the patient. The use of a valved conduit is recommended when an atrioventricular type of Fontan repair is planned in patients with tricuspid atresia, concordant ventriculo-arterial connexions and relatively large hypoplastic right ventricle.

Citations

Dec 1, 1991·Journal of the American College of Cardiology·D D MairG K Danielson
Jul 1, 1992·Journal of the American College of Cardiology·M A Fogel, A J Chin
Feb 6, 2004·The Journal of Thoracic and Cardiovascular Surgery·Amando GambaPaolo Ferrazzi
Jan 1, 1988·European Journal of Cardio-thoracic Surgery : Official Journal of the European Association for Cardio-thoracic Surgery·G CrupiL Parenzan
Sep 1, 1996·The Journal of Thoracic and Cardiovascular Surgery·R H FeldtG K Danielson
May 30, 1998·The Journal of Thoracic and Cardiovascular Surgery·L MertensM Gewillig
Feb 23, 2010·The Annals of Thoracic Surgery·Deepika ThackerJack Rychik
Sep 15, 1991·The American Journal of Cardiology·J RychikG Barber
Jan 15, 2014·International Journal of Cardiology·Timothy CottsUNKNOWN Alliance for Adult Research in Congenital Cardiology (AARCC)
May 8, 2002·Seminars in Thoracic and Cardiovascular Surgery. Pediatric Cardiac Surgery Annual·Jack Rychik, Thomas L Spray
Aug 4, 2001·Seminars in Thoracic and Cardiovascular Surgery. Pediatric Cardiac Surgery Annual·Jack Rychik
Jan 4, 2012·Journal of the American College of Cardiology·Jeffrey A FeinsteinGerard R Martin
Apr 21, 2012·Nutrition in Clinical Practice : Official Publication of the American Society for Parenteral and Enteral Nutrition·Jonathan N JohnsonPatrick W O'Leary
Jun 18, 2017·Journal of the American College of Cardiology·Maxim ItkinYoav Dori
Aug 21, 2003·Catheterization and Cardiovascular Interventions : Official Journal of the Society for Cardiac Angiography & Interventions·Ritu ChatrathDonald J Hagler
Oct 11, 2017·Circulation·George K LuiUNKNOWN American Heart Association Adult Congenital Heart Disease Committee of the Council on Clinical Cardiology and Council on Car
Apr 2, 2008·Congenital Heart Disease·Jack Rychik
Dec 3, 2016·European Respiratory Review : an Official Journal of the European Respiratory Society·Paul Clift, David Celermajer
Feb 1, 1997·Journal of Pediatric Gastroenterology and Nutrition·C SierraA Martinez-Valverde

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.