Protrusio acetabuli in Marfan syndrome: age-related prevalence and associated hip function

The Journal of Bone and Joint Surgery. American Volume
P D SponsellerHarry C Dietz

Abstract

Protrusio acetabuli is known to occur in patients with Marfan syndrome, but its prevalence, its effects on hip function, and its possible association with the subsequent development of degenerative hip disease have not been studied in a large population. Nevertheless, some clinicians have recommended prophylactic hip surgery for preadolescents with Marfan syndrome and protrusio acetabuli. We performed a cross-sectional study of 173 patients (346 hips) with Marfan syndrome who were interviewed and examined for calculation of the Iowa hip score. Anteroposterior radiographs of the pelvis were made, and two radiographic indices of acetabular depth were measured: (1) the center-edge angle of Wiberg and (2) the acetabular-ilioischial distance. The presence of protrusio was defined with use of two extant definitions: (1) a center-edge angle of >50 degrees or (2) an acetabular-ilioischial distance of >/=3 mm in male patients or >/=6 mm in female patients. Linear regression analyses were performed between these radiographic indices of acetabular depth and patient age, Iowa hip scores, the magnitude of the radiographic joint space, and range of motion. The prevalence of protrusio acetabuli was 27% according to the center-edge angle crite...Continue Reading

Citations

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Apr 20, 2011·The International Journal of Cardiovascular Imaging·Gwan Hyeop SohnDuk-Kyung Kim
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Sep 4, 2009·The Journal of the American Academy of Orthopaedic Surgeons·Eric D Shirley, Paul D Sponseller

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