Pulmonary atresia with intact ventricular septum and coronary cameral fistulae: an unusual finding of a subsystemic right ventricle

Cardiology in the Young
Shaun MohanAndrew C Glatz

Abstract

We report the case of a neonate with pulmonary atresia with intact ventricular septum and coronary cameral fistulae despite having a subsystemic right ventricle. We review the literature on coronary cameral fistulae in this disease and right ventricle-dependent coronary circulation. We discuss the potential consequences of this physiology, including risk of adverse cardiovascular events that may impact risk stratification and surgical palliation.

References

May 22, 2002·Journal of the American College of Cardiology·Piers E F DaubeneyUNKNOWN United Kingdom and Ireland Collaborative Study of Pulmonary Atresia with Intact Ventricular Septum
Aug 30, 2003·Pediatric Cardiology·S E SelametW M Gersony
Mar 31, 2004·The Journal of Thoracic and Cardiovascular Surgery·David A AshburnUNKNOWN Congenital Heart Surgeons Study members
Mar 31, 2006·Catheterization and Cardiovascular Interventions : Official Journal of the Society for Cardiac Angiography & Interventions·Mazeni Alwi
Aug 26, 2014·The Annals of Thoracic Surgery·Eva W CheungAlejandro J Torres

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