PMID: 15230125Jul 3, 2004Paper

Pulmonary hypertension in patients with systemic scleroderma with CREST-syndrome and without it

Terapevticheskiĭ arkhiv
N A KaroliE E Orlova

Abstract

To study incidence rate and characteristics of pulmonary hypertension development in patients with systemic sclerosis (SS). The study included 31 SS patients (30 females, 1 male, age 33-75 years, mean age 47.7 +/- 1.7 years). Pulmonary hypertension occurred more frequently in SS patients with CREST-syndrome than in SS patients free of this syndrome. SS patients with CREST-syndrome had also more severe ventricular hypertrophy than ventricular dilation. Echocardiography proved to be a highly informative method for detection of pulmonary hypertension in patients with SS. The necessity of hemodynamical study in SS patients is emphasized.

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