PMID: 9658472Jul 11, 1998Paper

Rasmussen syndrome

Revista de neurologia
R CaraballoN Fejerman

Abstract

Rasmussen's encephalitis is a neurological disorder probably of immunological origin, characterized by intractable epilepsy, neurological deterioration and the presence of antibodies against R3 glutamate receptors. To present the experience of an Argentinian Paediatric Neurology Service during the past 7 years. We analyzed the clinical histories of 12 patients with RS as defined by the diagnostic criteria proposed by Hart et al. We evaluated the following parameters: neurological examination, neuropsychological assessment, types of crises, age of onset, frequency, distribution, electroencephalogram, video EEG, evoked potentials, neuro-radiological studies; CT and cerebral MR using gadolinium, SPECT, lumbar puncture and cerebral biopsy. The crises were of simple partial motor type in 12 cases, secondarily generalized partial crises in 7 cases, complex partial crises in 4 cases and partial and generalized motor states in 8 cases. RESULTS. The ictal EEGs during the continuous partial crises showed contralateral focal slow activity of the affected side of the body in 30% of cases. The neuro-radiological studies (CT and MR) showed signs of cerebral hemiatrophy in all 12 cases, hyper-intense images in the T2 sequences of the fronto-t...Continue Reading

Related Concepts

Related Feeds

Autoimmune Diseases

Autoimmune diseases occur as a result of an attack by the immune system on the body’s own tissues resulting in damage and dysfunction. There are different types of autoimmune diseases, in which there is a complex and unknown interaction between genetics and the environment. Discover the latest research on autoimmune diseases here.

Related Papers

Archives of Neurology
R S McLachlanH Reichman
Epileptic Disorders : International Epilepsy Journal with Videotape
Laura KupilaReetta Kälviäinen
Nigerian Journal of Clinical Practice
C O Dawodu, D D Akinbo
Arquivos de neuro-psiquiatria
L C Coral, L J Haas
© 2022 Meta ULC. All rights reserved