Remission of seizures with immunosuppressive therapy in Parry-Romberg syndrome and en coup de sabre linear scleroderma: Case report and brief review of the literature

Pediatric Dermatology
L Elizabeth AndersonAndrea M Knight

Abstract

Parry-Romberg syndrome (PRS) is characterized by progressive atrophy of facial skin, soft tissues, muscle, and bone. En coup de sabre syndrome is a form of linear scleroderma (LS) involving the skin of the frontoparietal forehead and scalp. Both conditions can be associated with neurologic findings, including seizures. We explore a case in which skin findings and seizure burden improved with methotrexate therapy.

References

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Aug 28, 2002·Neurology·Anna PichiecchioFederico Zappoli
Oct 26, 2006·Scandinavian Journal of Rheumatology·A Holl-WiedenH J Girschick
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Jul 17, 2015·Medicine·Justine VixJean-Philippe Neau

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Citations

May 3, 2019·Journal of Medical Case Reports·Jimmy Girgis William AbdelnourZiryab Imad Taha Mahmoud
Nov 2, 2019·Paediatric Drugs·Ivan Foeldvari
Jun 28, 2020·Current Rheumatology Reports·Francesco Zulian, Francesca Tirelli
Jun 17, 2020·The Journal of Rheumatology·Ryan T LewinsonNadia J Luca
Sep 10, 2020·Frontiers in Neurology·Ling LongWei Qiu
Feb 12, 2020·Seizure : the Journal of the British Epilepsy Association·Ruben Rocha, Marios Kaliakatsos
Jul 18, 2021·Pediatric Dermatology·Jacquelyn R Sink, Yvonne E Chiu
Aug 7, 2021·Neurological Sciences : Official Journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology·Maha JamoussiMohamed Fredj

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