PMID: 14580655Oct 29, 2003Paper

Sickle cell anemia with moyamoya disease: outcomes after EDAS procedure

Pediatric Neurology
Robert H FryerNeil A Feldstein


Moyamoya disease is a relatively uncommon neurovascular complication of sickle cell anemia. We report a case series of six patients with sickle cell anemia who developed moyamoya disease and underwent encephaloduroarteriosynangiosis procedures. These six patients presented with either cerebrovascular accidents, transient ischemic attacks, or seizures, and subsequent magnetic resonance imaging scans were suggestive of moyamoya-like changes in the cerebral vasculature. Conventional cerebral angiography was used to confirm the diagnosis in all six patients. Four of six patients manifested a cerebrovascular accident before surgery, and two of these patients were compliant on a transfusion protocol at the time of their cerebrovascular accident. Bilateral (n = 4) or unilateral (n = 2) encephaloduroarteriosynangiosis procedures were performed without any complications. The patient who was stroke-free preoperatively had a cerebrovascular accident 2 weeks after the procedure; otherwise, all patients have remained free of neurovascular complications with an average follow-up of 33 months. Collateral anastomoses between external and internal carotid arteries were established by magnetic resonance angiography in three patients. The encepha...Continue Reading


Jan 1, 1978·Stroke; a Journal of Cerebral Circulation·K H MerkelM J Post
Nov 1, 1992·Neurologia Medico-chirurgica·Y Goto, Y Yonekawa
Jan 1, 1990·Pediatric Neurosurgery·E M Goldstein, H S Singer
Mar 1, 1989·Neurology·I ProhovnikD C De Vivo
Sep 1, 1987·Stroke; a Journal of Cerebral Circulation·T TagawaT Sawada
Jan 1, 1986·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·K FujitaS Matsumoto
Apr 1, 1974·Journal of Neurology, Neurosurgery, and Psychiatry·G Poór, G Gács
Oct 26, 1972·The New England Journal of Medicine·J A StockmanF A Oski
Jan 1, 1970·Brain : a Journal of Neurology·G E SolomonS Carter
Dec 1, 1982·Surgical Neurology·R Garza-Mercado
Jan 1, 1995·Pediatric Neurosurgery·P D Adelson, R M Scott
Dec 1, 1994·Acta Paediatrica Japonica; Overseas Edition·T SarenurO Tugrul
Aug 1, 1994·Mayo Clinic Proceedings·K UekiJ F Mellinger
Nov 1, 1993·Anesthesia and Analgesia·S G SorianoR M Scott
Nov 6, 1993·BMJ : British Medical Journal·B G Neville
Nov 1, 1993·Radiographics : a Review Publication of the Radiological Society of North America, Inc·B J Wiegel, G T Chua
Oct 2, 1993·BMJ : British Medical Journal
Feb 1, 1997·Surgical Neurology·M Fukui
Nov 28, 1997·Postgraduate Medical Journal·M FarrugiaA M Saks
Dec 31, 1997·The American Journal of Emergency Medicine·P C FerreraH Swanson
Dec 31, 1997·Clinical Neurology and Neurosurgery·Y KuwabaraM Fukui
Dec 31, 1997·Clinical Neurology and Neurosurgery·Y MatsushimaK Hirakawa
Dec 31, 1997·Clinical Neurology and Neurosurgery·H NakashimaT Ohmoto
Nov 1, 1996·Neurologia Medico-chirurgica·K HoukinH Abe
Jun 1, 2000·Journal of Child Neurology·K Ikezaki
Feb 1, 2008·Brain and nerve = Shinkei kenkyū no shinpo·Koji Tokunaga, Isao Date

❮ Previous
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May 10, 2012·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·J NgV Ganesan
Jun 2, 2007·Journal of Thrombosis and Thrombolysis·Praveen Kumar GuptaJanaki Sudhakar Praharaju
Jul 29, 2004·Current Treatment Options in Neurology·Fenella J. Kirkham, Michael R. DeBaun
Jan 10, 2009·Indian Journal of Pediatrics·Andrew A Mallick, Vijeya Ganesan
May 5, 2007·Nature Clinical Practice. Neurology·Fenella J Kirkham
Jul 25, 2006·Blood·Margaret T LeeUNKNOWN STOP Study Investigators
Mar 21, 2008·Journal of Neurosurgery. Pediatrics·Todd C HankinsonRichard C E Anderson
Nov 30, 2012·Annual Review of Medicine·Adetola A Kassim, Michael R DeBaun
Mar 30, 2010·Acta neurochirurgica·Imran LiaquatPeter R Bullock
Oct 9, 2014·Blood Cells, Molecules & Diseases·Ross M FasanoMonica L Hulbert
Jul 29, 2010·Transfusion·Keith Quirolo
Mar 10, 2005·British Journal of Haematology·Carolyn Hoppe
Nov 27, 2010·Advances in Medical Sciences·M ArkuszewskiJ Krejza
Nov 1, 2005·Journal of Clinical Neuroscience : Official Journal of the Neurosurgical Society of Australasia·B Darwish, M Besser
Jun 16, 2017·British Journal of Neurosurgery·Alexander AlamriChristos M Tolias
May 3, 2014·Stroke; a Journal of Cerebral Circulation·Walter N KernanUNKNOWN American Heart Association Stroke Council, Council on Cardiovascular and Stroke Nursing, Council on Clinical Cardiology, and
Oct 23, 2010·Stroke; a Journal of Cerebral Circulation·Karen L FurieUNKNOWN American Heart Association Stroke Council, Council on Cardiovascular Nursing, Council on Clinical Cardiology, and Interdisci
Nov 10, 2009·Developmental Medicine and Child Neurology·Vijeya Ganesan
Jul 11, 2009·Expert Review of Cardiovascular Therapy·Despina Eleftheriou, Vijeya Ganesan
Nov 24, 2005·Hematology·Richard Lottenberg, Kathryn L Hassell
Feb 25, 2020·Journal of Child Neurology·Andrew R PinesRadhika Dhamija
Jun 21, 2013·Expert Review of Hematology·Jennifer Webb, Janet L Kwiatkowski
Nov 15, 2011·Expert Review of Hematology·John J StrouseVictor Urrutia

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