Sildenafil in pulmonary hypertension secondary to unilateral agenesis of pulmonary artery

Pediatric Cardiology
M A HamdanH K Najm

Abstract

Unilateral agenesis of the pulmonary artery (PA) is a rare anomaly that can lead to pulmonary hypertension (PHTN). We report the case of a 10-month-old female with agenesis of the left PA, ventricular septal defect, and patent ductus arteriosus who developed PHTN precluding surgical repair. The use of sildenafil decreased PA pressure and normalized pulmonary vascular resistance, after which surgery was successfully performed.

References

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Aug 6, 1998·The Annals of Thoracic Surgery·K ImanakaT Takemura
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Citations

Aug 26, 2009·Pediatric Cardiology·Alice J HuddlestonEric S Ebenroth
Feb 8, 2014·The Journal of Thoracic and Cardiovascular Surgery·Carlos M MeryHenri Justino

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