Spontaneous Splenic Rupture in Vascular Ehlers-Danlos Syndrome

Vascular and Endovascular Surgery
Nayara Cioffi BataginiLee Kirksey

Abstract

Vascular Ehlers-Danlos Syndrome (VEDS) is a rare autosomal dominant collagen vascular disorder. Different from other Ehler-Danlos Syndrome subtypes, VEDS has poor prognosis due to severe fragility of connective tissues and association with life-threatening vascular and gastrointestinal complications. Spontaneous splenic rupture is a rare but hazardous complication related to this syndrome. To date, only 2 cases have been reported in the literature. Here we present another case of this uncommon complication, occurring in a 54-year-old woman in clinical follow-up for VEDS who presented with sudden onset of abdominal pain and hypotension.

References

Mar 1, 1985·Postgraduate Medical Journal·S C HarrisC A Austin
Mar 9, 2000·The New England Journal of Medicine·M PepinP H Byers
May 23, 2002·Annals of Vascular Surgery·Dominique P Germain
May 7, 2004·Annales de génétique·Dominique P Germain, Yessica Herrera-Guzman
Mar 1, 2005·Forensic Science International : Synergy·Michael Tsokos, Andreas Erbersdobler
Jul 14, 2005·Journal of Vascular Surgery·Gustavo S OderichPeter Gloviczki
Dec 19, 2006·Perspectives in Vascular Surgery and Endovascular Therapy·Gustavo S Oderich
Jul 21, 2007·Orphanet Journal of Rare Diseases·Dominique P Germain
Sep 23, 2008·Annals of Vascular Surgery·Arianne C van BonGeert J Wanten
Jan 10, 2009·Surgery Today·Antonio PriviteraAlastair Windsor
May 7, 2013·The Journal of Biological Chemistry·Kazunori MizunoHans Peter Bächinger
Jun 12, 2013·Annals of Surgery·David BergqvistAnders Wanhainen
Nov 30, 2013·The American Journal of Emergency Medicine·Anupam LalNiranjan Khandelwal
Mar 22, 2014·Journal of Vascular Surgery·Sherene ShalhubNazli B McDonnell

❮ Previous
Next ❯

Methods Mentioned

BETA
dissection
dissections

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.

Related Papers

The Journal of Emergency Medicine
Michael Levine, Jonathan Adler
RöFo : Fortschritte auf dem Gebiete der Röntgenstrahlen und der Nuklearmedizin
A HanschW A Kaiser
© 2021 Meta ULC. All rights reserved