PMID: 8940741Nov 1, 1996Paper

Steroid-responsive Rosai-Dorfman disease

Pediatric Hematology and Oncology
J I AntoniusA Baez-Giangreco

Abstract

Nodular skin lesions on the lateral aspects of the legs of a female child were first noticed at the age of 6 days. A biopsy of the lesions was done at the age of 6 months when the child had also developed cervical and inguinal lymphadenopathy and angiomatous lesions on the face. The diagnosis of Rosai-Dorfman disease (RDD; also known as sinus histiocytosis with massive lymphadenopathy, SHML) was made. Increasing respiratory obstruction by lymphoid tissue prompted a 2-week trial with oral prednisolone. A dramatic response occurred, with complete resolution of all clinical findings within 5 days, but with recurrence of lymphadenopathy 6 weeks after stopping with medication. Further observations over the next 3 years established a consistent response to prednisolone and a pattern of steroid dependence.

References

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Citations

Jun 1, 2000·Spine·J P HollowellM H Whittaker
Aug 26, 2009·Neuropathology : Official Journal of the Japanese Society of Neuropathology·Yin WangChengchuan Jiang
May 18, 2006·Journal of Neurosurgery·Christopher M McPhersonFranco DeMonte
Feb 26, 2009·Strahlentherapie und Onkologie : Organ der Deutschen Röntgengesellschaft ... [et al]·Faycal El MajdoubMohammad Maarouf
Feb 18, 2016·Journal of Cancer Research and Therapeutics·Sourya Acharya, Samarth Shukla
Mar 12, 2010·The American Journal of the Medical Sciences·Yu-Chin WuShung-Shung Sun
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Apr 8, 2009·The Journal of Dermatology·Masahiro OkaChikako Nishigori
Nov 16, 2014·European Spine Journal : Official Publication of the European Spine Society, the European Spinal Deformity Society, and the European Section of the Cervical Spine Research Society·Sara SciaccaRohit Shetty
Jun 24, 2017·Journal of Cutaneous Medicine and Surgery·Anna E KinioMelanie Pratt
Dec 9, 2010·Rare Tumors·Munenori IdeHiroyuki Kuwano
Apr 19, 2013·American Journal of Clinical Pathology·Xuefeng ZhangJames Vardiman
Apr 10, 2013·Clinical Nuclear Medicine·S PadmaK Sanjay Babu
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Mar 2, 2011·Neurologia Medico-chirurgica·Takao FukushimaYoichi Katayama
Nov 21, 2008·Journal of Neuro-oncology·Archana HindujaJoseph C Landolfi

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