Supratentorial cystic hemangioblastoma with infratentorial extension--a unique location and a rare infant case

Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery
Ismail H Tekkök, Aydin Sav

Abstract

Supratentorial occurrence of hemangioblastoma is an exceedingly rare event. Even rarer is the occurrence of a supratentorial hemangioblastoma in infancy. We hereby report the case of an 18-month-old girl who presented with irritability, increasing head size, and an open fontanelle. MR scans demonstrated triventricular hydrocephalus and a cystic mass within the left lateral ventricle. There was an 18 x 15 x 13 mm enhancing nodule along the medial aspect of the cyst. The cystic mass was mainly supratentorial but there was a caudal extension through the tentorial incisura that compressed the cerebellum. At surgery, the content of the cyst was xanthochromic. Enhancing medial nodule was extremely vascular and was extirpated totally. The pathological diagnosis was reticular variant of hemangioblastoma. The child is well at 4 years of age. An extensive review of the English literature revealed only three such cases. All three cases survived the operation.

References

Nov 1, 1990·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·R KumarR A Jones
Jan 1, 1991·Journal of Computer Assisted Tomography·S NakasuJ Handa
Sep 1, 1990·AJR. American Journal of Roentgenology·P C BuetowS Done
Mar 1, 1990·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·S OiT S Chan
Aug 1, 1989·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·A AsaiL E Becker
Oct 1, 1989·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·E GalassiM T Nasi
Jun 1, 1988·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·C LaprasJ D Patet
Jul 1, 1986·Surgical Neurology·G ZuccaroJ Monges
Jan 1, 1986·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·K SakamotoY Tanaka
Dec 1, 1985·Neurosurgery·T Tomita, D G McLone
Jun 1, 1984·Journal of Neurosurgery·V K KhoslaS Mehta
Jan 1, 1995·Journal of Neurosurgery·B K Richmond, J H Schmidt
Sep 1, 1994·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·W R MurshidI Kanaan
Mar 1, 1994·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·M R BalestriniS Giombini
Jan 1, 1993·Acta neurochirurgica·C Di RoccoA Iannelli
Jul 1, 1993·Pediatric Neurosurgery·U C ReedA J Diament
Dec 24, 1997·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·C H RickertF Gullotta
Apr 16, 1998·Journal of Korean Medical Science·S K ChungB K Cho
Jan 8, 1999·Brain Tumor Pathology·T FurutaT Ohmoto
Dec 31, 2002·Pediatric Neurology·Hart Isaacs
May 7, 2003·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Roberto Rivera-LunaFernando Rueda-Franco
Aug 30, 2003·Archives of Pathology & Laboratory Medicine·Mustafa Fuat AcikalinFaruk Altinel
Sep 28, 2004·Journal of Child Neurology·Helen K Young, Heather Johnston

❮ Previous
Next ❯

Citations

Jul 24, 2012·Child's Nervous System : ChNS : Official Journal of the International Society for Pediatric Neurosurgery·Turkan PatirogluMustafa Akcakus
Dec 25, 2007·Journal of Neurosurgery·Hakan KarabagliBurak Durmaz

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.