Surdocardiac syndrome of Jervell and Lange-Nielsen, with prolonged QT interval present at birth, and severe anaemia and syncopal attacks in childhood.

British Heart Journal
A Langslet, S J Sorland

Abstract

A case of the surdocardiac syndrome of Jervell and Lange-Nielsen, with prolonged QT interval in the electrocardiogram at birth, is described. The affected girl presented 3 1/2 years later with severe iron deficiency anaemia, despite apparently adequate nutrition. At the age of 4 1/2 years she had a sudden attack of unconsciousness. Treatment with the beta-adrenoceptor blocker practolol was started and 3 years after initiation of this treatment she has been free from syncopal attacks. The QT interval remains prolonged. Her brother also had severe iron deficiency anaemia and had several attacks of unconsciousness before he died suddenly at the age of 3 1/2 years.

Citations

Nov 22, 2002·International Journal of Pediatric Otorhinolaryngology·R ChorbachiC H Raine
Jul 1, 1991·International Journal of Pediatric Otorhinolaryngology·F CusimanoC Rizzo

❮ Previous
Next ❯

Related Concepts

Related Feeds

Anemia

Anemia develops when your blood lacks enough healthy red blood cells. Anemia of inflammation (AI, also called anemia of chronic disease) is a common, typically normocytic, normochromic anemia that is caused by an underlying inflammatory disease. Here is the latest research on anemia.

Related Papers

International Journal of Pediatric Otorhinolaryngology
F CusimanoC Rizzo
International Journal of Cardiology
B KomsuoğluS S Komsuoğlu
© 2022 Meta ULC. All rights reserved