Surgical and anesthetic management for hepatectomy in two pediatric patients with trisomy 18, pulmonary hypertension, and hepatoblastoma

Pediatric Blood & Cancer
Donald J LucasAngela Trobaugh-Lotrario

Abstract

Children with trisomy 18 are surviving longer and undergoing more aggressive life-sustaining therapy. This report describes two patients with trisomy 18 and hepatoblastoma (HB) successfully resected in the setting of significant pulmonary hypertension. Forty-four previously published cases of the association between HB and trisomy 18 are reviewed. With careful multidisciplinary preoperative planning, successful resection of HB in children with trisomy 18 who have significant pulmonary hypertension is feasible. Because HB and trisomy 18 are increasing in prevalence, the need for timely liver tumor resection in the setting of pulmonary hypertension will be more common.

References

Oct 1, 1992·European Journal of Pediatric Surgery : Official Journal of Austrian Association of Pediatric Surgery ... [et Al] = Zeitschrift Für Kinderchirurgie·K TanakaK Ozawa
May 1, 1989·American Journal of Medical Genetics·V MamlokR Mamlok
May 1, 1987·American Journal of Medical Genetics·M Dasouki, M Barr
Mar 1, 1996·Pediatric Pathology & Laboratory Medicine : Journal of the Society for Pediatric Pathology, Affiliated with the International Paediatric Pathology Association·K E BoveF Ryckman
Mar 1, 1997·Journal of Clinical Oncology : Official Journal of the American Society of Clinical Oncology·J M Van TornoutJ A Ortega
Sep 1, 1997·Pediatric Hematology and Oncology·M TeraguchiY Kobayashi
May 8, 2001·World Journal of Surgery·S E JungW K Kim
May 31, 2001·Pediatrics International : Official Journal of the Japan Pediatric Society·K MaruyamaT Koizumi
Apr 3, 2003·Pediatrics·Sonja A RasmussenJ M Friedman
Mar 11, 2006·American Journal of Medical Genetics. Part a·Robert Roger LebelDaniel L Van Dyke
Jun 20, 2006·Journal of Clinical Oncology : Official Journal of the American Society of Clinical Oncology·Marcio H MalogolowkinRobert P Castleberry
Jul 27, 2007·Pediatric Surgery International·Kohei TakadaYasuo Kamiyama
Mar 25, 2009·International Journal of Infectious Diseases : IJID : Official Publication of the International Society for Infectious Diseases·Ridvan DuranMuzaffer Demir
Oct 16, 2009·Journal of Medical Case Reports·Lidija KitanovskiJanez Jazbec
Apr 4, 2012·Journal of Pediatric Hematology/oncology·Elaine Maria PereiraRosanna Ricafort
May 29, 2012·Pediatrics International : Official Journal of the Japan Pediatric Society·Shota UekusaHideo Mugishima
Jul 9, 2013·The Lancet Oncology·József ZsirosUNKNOWN International Childhood Liver Tumours Strategy Group (SIOPEL)
Aug 27, 2013·European Journal of Pediatrics·Zhen Han TanAh Moy Tan
Jul 31, 2016·American Journal of Medical Genetics. Part C, Seminars in Medical Genetics·Daniel SatgéMichel Vekemans
Sep 13, 2016·Journal of Pediatric Genetics·Leonardo I ValentinPrakash Masand
Oct 20, 2017·Pediatrics·Katherine A KosivR Thomas Collins
Apr 28, 2018·Pediatric Blood & Cancer·Akiko InoueHiroshi Tamai

❮ Previous
Next ❯

Citations

Aug 10, 2021·Frontiers in Oncology·Huitong ChenZhenjian Zhuo

❮ Previous
Next ❯

Related Concepts

Trending Feeds

COVID-19

Coronaviruses encompass a large family of viruses that cause the common cold as well as more serious diseases, such as the ongoing outbreak of coronavirus disease 2019 (COVID-19; formally known as 2019-nCoV). Coronaviruses can spread from animals to humans; symptoms include fever, cough, shortness of breath, and breathing difficulties; in more severe cases, infection can lead to death. This feed covers recent research on COVID-19.

Blastomycosis

Blastomycosis fungal infections spread through inhaling Blastomyces dermatitidis spores. Discover the latest research on blastomycosis fungal infections here.

Nuclear Pore Complex in ALS/FTD

Alterations in nucleocytoplasmic transport, controlled by the nuclear pore complex, may be involved in the pathomechanism underlying multiple neurodegenerative diseases including Amyotrophic Lateral Sclerosis and Frontotemporal Dementia. Here is the latest research on the nuclear pore complex in ALS and FTD.

Applications of Molecular Barcoding

The concept of molecular barcoding is that each original DNA or RNA molecule is attached to a unique sequence barcode. Sequence reads having different barcodes represent different original molecules, while sequence reads having the same barcode are results of PCR duplication from one original molecule. Discover the latest research on molecular barcoding here.

Chronic Fatigue Syndrome

Chronic fatigue syndrome is a disease characterized by unexplained disabling fatigue; the pathology of which is incompletely understood. Discover the latest research on chronic fatigue syndrome here.

Evolution of Pluripotency

Pluripotency refers to the ability of a cell to develop into three primary germ cell layers of the embryo. This feed focuses on the mechanisms that underlie the evolution of pluripotency. Here is the latest research.

Position Effect Variegation

Position Effect Variagation occurs when a gene is inactivated due to its positioning near heterochromatic regions within a chromosome. Discover the latest research on Position Effect Variagation here.

STING Receptor Agonists

Stimulator of IFN genes (STING) are a group of transmembrane proteins that are involved in the induction of type I interferon that is important in the innate immune response. The stimulation of STING has been an active area of research in the treatment of cancer and infectious diseases. Here is the latest research on STING receptor agonists.

Microbicide

Microbicides are products that can be applied to vaginal or rectal mucosal surfaces with the goal of preventing, or at least significantly reducing, the transmission of sexually transmitted infections. Here is the latest research on microbicides.

Related Papers

The British Journal of Clinical Practice
G R SeabrookB J Britton
Pediatrics International : Official Journal of the Japan Pediatric Society
Shota UekusaHideo Mugishima
© 2022 Meta ULC. All rights reserved