Surgical Management and Outcomes of Ebstein Anomaly in Neonates and Infants: A Society of Thoracic Surgeons Congenital Heart Surgery Database Analysis

The Annals of Thoracic Surgery
Kimberly A HolstMarshall L Jacobs

Abstract

Ebstein anomaly (EA) encompasses a broad spectrum of morphology and clinical presentation. Those who are symptomatic early in infancy are generally at highest risk, but there are limited data regarding multicentric practice patterns and outcomes. We analyzed multiinstitutional data concerning operations and outcomes in neonates and infants with EA. Index operations reported in The Society of Thoracic Surgeons Congenital Heart Surgery Database (2010 to 2016) were potentially eligible for inclusion. Analysis was limited to patients with diagnosis of EA and less than 1 year of age at time of surgery (neonates ≤30 days, infants 31 to 365 days). The study population included 255 neonates and 239 infants (at 95 centers). Among neonates, median age at operation was 7 days (interquartile range, 4 to 13 days) and the majority required preoperative ventilation (61.6%, n = 157). The most common primary operation performed among neonates was Ebstein repair (39.6%, n = 101), followed by systemic-to-pulmonary shunt (20.4%, n = 52) and tricuspid valve closure (9.4%, n = 24). Overall neonatal operative mortality was 27.4% (n = 70), with composite morbidity-mortality of 51.4% (n = 48). For infants, median age at operation was 179 days (interqua...Continue Reading

Citations

Dec 15, 2019·World Journal for Pediatric & Congenital Heart Surgery·Thomas MartensThierry Bové
Jun 5, 2019·Interactive Cardiovascular and Thoracic Surgery·Carles Bautista-RodriguezOliver Ghez
Dec 15, 2020·Interactive Cardiovascular and Thoracic Surgery·Laura HomzovaAntonia Schulz
Feb 20, 2021·Indian Journal of Thoracic and Cardiovascular Surgery : Official Organ, Association of Thoracic and Cardiovascular Surgeons of India·T K Susheel Kumar
Apr 30, 2020·Journal of Veterinary Cardiology : the Official Journal of the European Society of Veterinary Cardiology·V ChetboulL Desquilbet

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