PMID: 15241223Jul 9, 2004Paper

Susac syndrome

Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology
Menachem GrossTamir Ben-Hur

Abstract

The objective of this study was to describe the clinical manifestations; radiographic, audiometric, and retinal fluorescein angiography findings; pathogenesis and treatment of Susac syndrome with review of the literature. We conducted a retrospective case review. This study was conducted at a tertiary referral center. A 50-year-old woman presented with recurrent episodes of neurologic symptoms, bilateral sensorineural hearing loss, and silent retinal artery occlusion. The patient underwent complete evaluation, including magnetic resonance image studies, audiometric tests, and retinal fluorescein angiography. She was treated initially with corticosteroids and later with other immunosuppressive agents. The patient was initially diagnosed with left sudden sensorineural hearing loss. Despite comprehensive clinical and laboratory studies that did not reveal systemic disease, 3 weeks later, the patient developed vertigo, sensorineural hearing loss, and tinnitus in the opposite ear. The neurologic involvement and the bilateral audiologic manifestations raised the possibility of Susac syndrome. Susac syndrome is a rare disorder of unknown origin characterized by the triad of encephalopathy, fluctuating hearing loss, and visual loss res...Continue Reading

References

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Citations

Nov 26, 2010·Journal of Neurology·Dipender GillJacqueline Palace
Dec 25, 2008·Otology & Neurotology : Official Publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology·Michelle M RoeserMichael B Gluth
Apr 17, 2007·Medicine·Fleur Aubart-CohenThomas Papo
Oct 17, 2009·European Archives of Oto-rhino-laryngology : Official Journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : Affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery·Roberto BovoAlessandro Martini
Jan 2, 2009·The Laryngoscope·Brianna K CrawleyJeffrey P Harris
Jul 9, 2011·Acta Oto-laryngologica·Aline Gomes BittencourtRicardo Ferreira Bento
Jul 23, 2020·Journal of Neurology·Todd A HardyG Michael Halmagyi
May 14, 2005·Current Opinion in Neurology·Menachem Gross, Ron Eliashar
Sep 25, 2020·Current Opinion in Ophthalmology·Yael Redler, Bart K Chwalisz
Oct 3, 2018·Immunologic Research·Francesca Yoshie RussoAntonio Greco
May 1, 2013·Nature Reviews. Neurology·Jan DörrIlka Kleffner
Oct 4, 2020·Current Opinion in Ophthalmology·Yael Redler, Bart K Chwalisz

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