Systemic lupus erythematosus presenting with mixed-type fulminant autoimmune hemolytic anemia

Pediatrics International : Official Journal of the Japan Pediatric Society
Yoko HiranoAkira Oka

Abstract

We report the case of a 9-year-old girl who presented with mixed-type fulminant autoimmune hemolytic anemia (AIHA) at the onset of systemic lupus erythematosus (SLE). On admission, laboratory investigations indicated very severe anemia (Hb, 2.7 g/dL) with reticulocytosis and positive direct/indirect Coombs tests. In addition, agglutinative reaction was clinically observed. Based on further examinations, the patient was diagnosed with AIHA complicated with SLE, and mixed-type AIHA was clinically identified. With oral prednisolone and methylprednisolone pulse therapy, the patient entered remission.

References

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Citations

Aug 27, 2016·Immunologic Research·Paola Ester López-DíazHonorio Torres-Aguilar
May 26, 2021·Neonatology·Shunsuke YamamotoShouichi Ohga

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