The Lecompte maneuver for relief of airway compression in absent pulmonary valve syndrome

The Annals of Thoracic Surgery
Lars NölkeTom R Karl

Abstract

Congenital absence of the pulmonary valve syndrome (APVS) is a rare cardiac defect characterized by aneurysmal pulmonary arteries, hypoplastic pulmonary valve cusps, and tracheobronchial abnormalities. Absence of the pulmonary valve syndrome usually occurs in conjunction with ventricular septal defect (VSD) and right ventricular outflow tract obstruction (RVOTO). Surgical mortality rates as high as 16% to 56% have been reported. Here, we describe the surgical results using the Lecompte maneuver, reduction pulmonary arterioplasty, and a valved right ventricle to pulmonary artery (RV-PA) conduit. Medical records and operative and echocardiography reports for all surgical APVS cases were retrospectively examined for pertinent clinical variables. A patient with left bronchial compression due to enlarged pulmonary arteries associated with totally anomalous pulmonary venous drainage (TAPVD) is included to illustrate the value of the Lecompte maneuver. From January 2002 to December 2004, 4 children with APVS had surgery at a median age of 5 months (range, 3 months to 3.5 years). Three had malalignment VSD and RVOTO. Four had respiratory signs (cough, wheeze, tachypnea, oxygen dependence, ventilator dependence), and all 5 had evidence ...Continue Reading

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Citations

Feb 27, 2013·Interactive Cardiovascular and Thoracic Surgery·Renjie HuWenxiang Ding
Aug 6, 2013·The Annals of Thoracic Surgery·Mauro Lo RitoWilliam J Brawn
Feb 5, 2013·The Journal of Heart and Lung Transplantation : the Official Publication of the International Society for Heart Transplantation·Erin L AlbersDebra A Dodd
Jun 3, 2008·Paediatric Respiratory Reviews·Clare A McLarenDerek J Roebuck
Sep 30, 2015·Clinical Research in Cardiology : Official Journal of the German Cardiac Society·J GrohmannR Höhn
Jan 3, 2014·Cardiology in the Young·Anastasia Martinez-Esteve MelnikovaPatrick O Myers
Mar 29, 2014·World Journal for Pediatric & Congenital Heart Surgery·Sachin TalwarBalram Airan
Sep 10, 2019·World Journal for Pediatric & Congenital Heart Surgery·Christina L GreeneFrank L Hanley
Sep 15, 2021·World Journal for Pediatric & Congenital Heart Surgery·Jaymie VarenbutOsami Honjo

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