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The role of genetics in pulmonary arterial hypertension

The Journal of Pathology

Oct 23, 2016

Lijiang Ma, Wendy K Chung

Abstract

Group 1 pulmonary hypertension or pulmonary arterial hypertension (PAH) is a rare disease characterized by proliferation and occlusion of small pulmonary arterioles, leading to progressive elevation of pulmonary artery pressure and pulmonary vascular resistance, and right ventricular fa...read more

Mentioned in this Paper

Recombinant Transforming Growth Factor
CAV1 gene
Pulmonary Arterial Hypertension
2-oxo-hept-3-ene-1,7-dioate Hydratase Activity
Transforming Growth Factor beta
Bone morphogenetic protein receptor type II
Clinical Management
SMAD9
Lung
Genes
2
1
51
Paper Details
References
  • References82
  • Citations9
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  • References82
  • Citations9
1

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The role of genetics in pulmonary arterial hypertension

The Journal of Pathology

Oct 23, 2016

Lijiang Ma, Wendy K Chung

PMID: 27770446

DOI: 10.1002/path.4833

Abstract

Group 1 pulmonary hypertension or pulmonary arterial hypertension (PAH) is a rare disease characterized by proliferation and occlusion of small pulmonary arterioles, leading to progressive elevation of pulmonary artery pressure and pulmonary vascular resistance, and right ventricular fa...read more

Mentioned in this Paper

Recombinant Transforming Growth Factor
CAV1 gene
Pulmonary Arterial Hypertension
2-oxo-hept-3-ene-1,7-dioate Hydratase Activity
Transforming Growth Factor beta
Bone morphogenetic protein receptor type II
Clinical Management
SMAD9
Lung
Genes
2
1
51

Similar Papers Found In These Feeds

Related Papers

Paper Details
References
  • References82
  • Citations9
12345...
  • References82
  • Citations9
1
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