The United States registry for fibromuscular dysplasia: new findings and breaking myths

Techniques in Vascular and Interventional Radiology
Aditya M Sharma, Bryan Kline

Abstract

Fibromuscular dysplasia (FMD) is a nonatherosclerotic, noninflammatory arterial disease predominantly seen in women. Most FMD cases are classified as medial fibroplasia, which has the appearance of a string of beads on angiography. Until recently, FMD was thought to be seen in women in their 20s and 30s, with more than 60%-75% of cases occurring in the renal artery and 25% of cases in the carotid artery. Hypertension was regarded as the primary symptom seen in these patients followed by a small number of patients presenting with intracranial aneurysms with subarachnoid hemorrhage. The United States Registry of FMD, a patient registry, has broken many preconceived notions as well as provided more in-depth knowledge of this uncommon disorder. In this review, we discuss the findings of this registry and its use in understanding this disorder. In addition to the registry, we review other recent studies and future directions in the diagnosis and management of this disorder.

References

Apr 30, 2004·The New England Journal of Medicine·David P Slovut, Jeffrey W Olin
Mar 3, 2007·Journal of Human Hypertension·J PerduX Jeunemaitre

❮ Previous
Next ❯

Citations

Feb 3, 2016·International Journal of Cardiology·Christa E KuckEva Kline-Rogers
Mar 13, 2016·The Journal of Clinical Hypertension·Elias A SanidasVasilios Papademetriou
Oct 16, 2015·Vascular and Endovascular Surgery·Nassir RostambeigiJames Kyle Anderson
Aug 30, 2018·European Journal of Clinical Investigation·Patricia Van der NiepenAlexandre Persu
Aug 10, 2016·Hypertension·Alexandre PersuUNKNOWN Working Group “Hypertension and the Kidney” of the European Society of Hypertension and the European Fibromuscular Dysplasia
Jul 7, 2017·Neurology. Clinical Practice·Andrea M HarriottGuy A Rordorf
Jun 9, 2018·International Journal of Molecular Sciences·Silvia Di MonacoAlexandre Persu
Dec 30, 2016·Oxford Medical Case Reports·Kevin Y C SuBrendan P W Kaufman
Aug 18, 2018·Vascular and Endovascular Surgery·Kara A RothenbergJordan R Stern
May 28, 2019·Acta neurologica Belgica·Hiroshi YokotaHiroyuki Hashimoto
Dec 17, 2020·Interventional Neuroradiology : Journal of Peritherapeutic Neuroradiology, Surgical Procedures and Related Neurosciences·S MathewJ Kovoor
Aug 29, 2019·Radiology. Cardiothoracic Imaging·Michael A WinklerMary Sheppard

❮ Previous
Next ❯

Related Concepts

Related Feeds

Basal Ganglia Cerebrovascular Disease

Basal ganglia cerebrovascular disease is a condition where the blood vessels in the basal ganglia are damaged or malfunction. Discover the latest research on basal ganglia cerebrovascular disease here.

Aneurysm

Aneurysms are outward distensions or bulges that occurs in a weakened wall of blood vessels. Discover the latest research on aneurysms here.

Basal Ganglia

Basal Ganglia are a group of subcortical nuclei in the brain associated with control of voluntary motor movements, procedural and habit learning, emotion, and cognition. Here is the latest research.