Tracheobronchial prosthesis in Mounier-Kuhn syndrome: New perspectives

Revue des maladies respiratoires
M SauvageJ-M Vergnon

Abstract

Mounier-Kuhn syndrome or tracheobronchomegaly is a rare congenital condition, the management of which is complex. We report the case of a patient who was treated with interventional endoscopy. We describe the case of a 74-year-old man with a diagnosis of tracheobronchomegaly who was admitted in 2003 with a background of deteriorating respiratory status and the occurrence of postural syncope. He initially received a tracheobronchial silicone Y prosthesis, extended with metal prostheses at the tracheal and bronchial level. This arrangement remained stable until 2011. He then began to develop episodes of asphyxia related to posterior dislocation of the tracheobronchial prosthesis, after breakage of the metallic mesh tracheal prosthesis. A new tracheobronchial prosthesis Y was then placed, custom-made from a 3D model of the airways. This was clinically and functionally effective. This case describes the management of a patient with Mounier-Kuhn syndrome by interventional bronchoscopy, with the adaptation of prosthetic materials, on an individual basis, to the anatomy of the patient's airway.

References

Mar 30, 2007·The European Respiratory Journal·L FreitagC H Marquette
Nov 27, 2007·The Annals of Thoracic Surgery·Septimiu D Murgu, Henri G Colt
Mar 8, 2011·The Annals of Thoracic Surgery·Sidhu P GangadharanMalcolm M DeCamp
Oct 20, 2011·Journal of Thoracic Imaging·Carole A RidgePhillip M Boiselle
Dec 12, 2012·Revue des maladies respiratoires·H DutauP Astoul

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