PMID: 2507210Oct 1, 1989Paper

Transcultural understanding of a hereditary disorder. Mucopolysaccharidosis VI in a Vietnamese family

Clinical Pediatrics
L HandelmanI M Eisenbruch

Abstract

A case study of a family referred for clarification of cultural issues illustrates how a transcultural psychiatric service developed in the pediatric hospital setting can be used to advantage. A Vietnamese family with an inherited disorder. Mucopolysaccharidosis type VI (Maroteaux-Lamy syndrome, MPS VI), resisted genetic counseling and contraception. Three out of their six children were affected, one with a fatal outcome. The transcultural consultation offered an understanding of their behavior and facilitated subsequent management.

References

Apr 1, 1977·Culture, Medicine and Psychiatry·B J Good
Jun 1, 1987·Clinical Cardiology·L V FongC W Chow
Jun 1, 1987·Journal of the Royal Society of Medicine·S Menahem
Oct 1, 1983·The British Journal of Psychiatry : the Journal of Mental Science·M Eisenbruch
Sep 1, 1980·General Hospital Psychiatry·R K RiesM A Schuckit

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Citations

Aug 1, 1991·Acta Paediatrica Japonica; Overseas Edition·Y ShigematsuK Konishi
Jul 4, 2001·Journal of Medical Genetics·B MeiserD Goldstein
Mar 4, 2000·Child: Care, Health and Development·S Menahem, G Halasz

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