Uncommon presentation of adult-form scimitar syndrome associated with single left pulmonary vein in a pregnant woman

BMJ Case Reports
Sarah Ali AlthomaliMohammad Salih Almalki

Abstract

Scimitar syndrome is the constellation of malformations including an abnormal venous drainage of the right lung into the inferior vena cava, associated with the right lung and systemic supply to the right lung. The anomalous vein looks like the curved, Turkish sword (scimitar), hence the name.The adult form of scimitar syndrome is rare, and it is usually an incidental diagnosis based on the characteristic finding on radiological imaging since the patients are usually asymptomatic or with minimal symptoms.Our patient presented with a rare presentation of scimitar syndrome, which is tachyarrhythmia (sinus tachycardia, with episodes of supraventricular tachycardia). The diagnosis of scimitar syndrome was made based on the typical radiological finding of the anomalous venous drainage on CT angiography. Our patient does not have the full spectrum of the scimitar syndrome; therefore, she did not suffer from the usual complication (pulmonary hypertension). She was treated with ablation without surgical intervention.

References

Aug 15, 1992·The American Journal of Cardiology·C DupuisG Helmius
Feb 1, 1995·The European Respiratory Journal·F M SchramelJ M van den Bosch
Jul 1, 1968·Circulation·H A SnellenE C Hoefsmit
Nov 27, 2007·The Annals of Thoracic Surgery·Bahaaldin AlsoufiJohn G Coles
May 12, 2009·International Journal of Gynaecology and Obstetrics : the Official Organ of the International Federation of Gynaecology and Obstetrics·Jason D BellLawrence D Devoe
May 11, 2011·Respiration; International Review of Thoracic Diseases·Mateo Porres-AguilarC Gregory Elliott
Nov 22, 2011·Journal of the Chinese Medical Association : JCMA·Shiang-Fen HuangYu-Chin Lee
Oct 4, 2012·Chest·Antoine LegrasJean-François Régnard
Feb 15, 2013·Sexually Transmitted Diseases·Kwame Owusu-EduseiHarrell W Chesson
Feb 20, 2014·Archives of Gynecology and Obstetrics·Mehmet Aytac YukselRiza Madazli
Jun 26, 2014·Indian Journal of Anaesthesia·Moira A Hendrie, Deepak Mathur
Oct 27, 2015·Indian Pediatrics·Sivasambo KalpanaNeville Ag Solomon

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Citations

Sep 25, 2021·Pediatrics International : Official Journal of the Japan Pediatric Society·Keiko FunataTakao Takahashi

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