Jun 15, 2011

Unusual presentation in Axenfeld-Rieger syndrome

Indian Journal of Ophthalmology
Rajul S ParikhRavi Thomas


We report an unusual presentation of a case of Axenfeld-Rieger (A-R) syndrome. A 14-year-old male presented with gradual dimness of vision for 1 year and redness of left eye for 3 days. The patient had megalocornea with Haab's striae in the right eye and posterior embryotoxon in both the eyes. In the left eye, there was a white cord-like structure traversing the anterior chamber with adhesions to iris tissue along its course. On two antiglaucoma medications, his intraocular pressure (IOP) was 22 mm Hg in the right eye and 18 mm Hg in the left eye. Gonioscopy revealed a cord-like structure originating at the level of Schwalbe's line. He underwent right eye trabeculectomy with mitomycin-C. This case highlights a rare presentation of a strange cord-like structure, a rare presentation of A-R syndrome.

  • References4
  • Citations1


  • References4
  • Citations1

Mentioned in this Paper

Antiglaucoma medications
Wernicke Aphasia
Hepatitis A
Anterior Chamber of Eye Structure
Entire Iris
Congenital Keratoglobus
Right Eye

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