PMID: 6110787Mar 1, 1981Paper

Urological implications of the beckwith-wiedemann syndrome

The Journal of Urology
W N Taylor

Abstract

A significant number of children with the Beckwith-Wiedemann syndrome are prone to the development of nephroblastomas and adrenal carcinomas. Renomegaly, a prolonged tubular blush on excretory urography similar to that of medullary sponge kidney, and previously undescribed caliceal diverticula may be observed. Diligent followup is mandatory to detect early neoplasia. Suggestions are detailed based on reported case management.

References

Apr 1, 1979·The Journal of Pediatrics·P A RaineP E Campbell

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Citations

Dec 1, 1991·The Australian and New Zealand Journal of Surgery·S Crankson, S Ahmed
Jan 1, 1987·Pediatric Radiology·J B Bronk, B R Parker
Jun 7, 2006·Fetal and Pediatric Pathology·L G BestJ M Opitz
Jul 13, 2005·Pediatric and Developmental Pathology : the Official Journal of the Society for Pediatric Pathology and the Paediatric Pathology Society·M Michael Cohen

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