Usefulness of magnetic resonance imaging for the diagnosis of right ventricular dysplasia in children

The American Journal of Cardiology
Mark A FogelLarry Rhodes

Abstract

Cardiac magnetic resonance (CMR) has been helpful in adults in the diagnosis of arrhythmogenic right ventricular dysplasia. Short of direct surgical observation or autopsy, no gold standard exists. CMR diagnostic criteria include right atrial and ventricular dilation, regional right ventricular (RV) wall motion abnormalities, outflow tract ectasia, and myocardial fatty infiltration. To determine whether adult diagnostic criteria are useful in children referred for CMR for this diagnosis, the images and records of 81 patients (aged 11.5 +/- 5.5 years) over an 8-year period were reviewed. Histories included ventricular tachycardia, palpitations, dilated right ventricle, syncope, near sudden death, or family history of RV dysplasia. Four families were studied with parents who had RV dysplasia diagnosed by surgery, explanted heart, or CMR. CMR imaging included T1-weighted imaging, cine, 1-dimensional RV myocardial tagging, and phase-encoded velocity mapping, and 2 patients underwent delayed-enhancement CMR. Only 1 of the 81 patients met 5 of the criteria. None of the others met >2 of the criteria, and only 2 patients met 1 or 2 criteria. For questionable regional wall motion abnormalities, RV myocardial tagging was helpful. In conc...Continue Reading

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Citations

May 10, 2008·Journal of Cardiovascular Magnetic Resonance : Official Journal of the Society for Cardiovascular Magnetic Resonance·Lars Grosse-WortmannShi-Joon Yoo
May 14, 2014·International Journal of Cardiology·Ying-Chieh LiaoShih-Ann Chen
Dec 17, 2014·Progress in Pediatric Cardiology·Angeliki AsimakiJeffrey E Saffitz
Mar 28, 2009·Heart Rhythm : the Official Journal of the Heart Rhythm Society·Robert M Hamilton, Lee Fidler
Jul 16, 2009·Pacing and Clinical Electrophysiology : PACE·Robert M Hamilton
Mar 15, 2015·Journal of the American College of Cardiology·Yousef EtoomLars Grosse-Wortmann
Sep 27, 2020·La Radiologia medica·Pierpaolo PalumboErnesto Di Cesare

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