When It Doesn't Fit: Congenital Anomalies of the Choledochus

European Journal of Pediatric Surgery Reports
Helena Reusens, Mark Davenport

Abstract

Introduction  Congenital choledochal malformations (CCMs) are characterized by intra- and/or extrahepatic bile duct dilatation. Five basic types (1-5) are recognized in Todani's classification and its modifications, of which types 1 and 4 typically have an associated anomalous pancreatobiliary junction and common channel (CC). We describe two cases with previously undescribed features. Case Report  1 Antenatal detection of a cyst at porta hepatis was made in an otherwise normal girl of Iranian parentage. She was confirmed to be a CCM (20 mm diameter), postnatally, with no evidence of obstruction. Surgical exploration was performed at 12 weeks. She had an isolated cystic dilatation of the right-hepatic duct only. The left-hepatic duct and common bile duct (CBD) were normal without a CC. Histology of the resected specimen showed stratified squamous epithelium. Case Report 2  A preterm (31 weeks of gestation) boy of Nigerian parentage was presented. His mother was HIV + ve and he was treated with nucleoside reverse transcriptase inhibitors following birth. He had persistent cholestatic jaundice and a dilated (10 mm) bile duct from birth. Although the jaundice resolved, the dilatation persisted and increased, coming to surgery aged...Continue Reading

References

Sep 1, 1991·The British Journal of Surgery·M DavenportE R Howard
Dec 13, 2005·Journal of Pediatric Surgery·Bill ChiuRiccardo A Superina
Feb 2, 2006·Pediatric Surgery International·Erica Makin, Mark Davenport
Feb 16, 2008·Digestive Diseases and Sciences·Leslie PriceNicholas Agoff
Jul 5, 2011·The British Journal of Surgery·C TurowskiM Davenport
Apr 27, 2016·Journal of Pediatric Surgery·Enrico La PergolaMark Davenport
May 17, 2017·International Journal of Surgical Pathology·Dong Hyang KwonMetin Ozdemirli
Nov 15, 2017·Pediatric Surgery International·Filippo Parolini, Mark Davenport

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