PMID: 4040692Jun 1, 1985

X-linked bulbo-spinal neuronopathy of late onset

Acta Neurologica Scandinavica
P MartinelliE Lugaresi


Two cases of X-linked bulbo-spinal neuronopathy (BSN) of late onset are presented. An extensive review of the literature shows that, in addition to the signs of a chronic degeneration of brainstem and spinal neurons, other clinical features may also be present at the onset of the disease, or develop during its course. Some clinical, electrophysiological and anatomical data support the hypothesis that BSN is not purely a motoneuronopathy but also concerns sensory nerve.


Jul 1, 1978·Muscle & Nerve·S P RingelH A Lubs
Apr 1, 1975·Journal of the Neurological Sciences·C StefanisC P Panayiotopoulos
Jan 1, 1968·Acta Neurologica Scandinavica·H A PetersH H Reese
Feb 1, 1966·Journal of Neurology, Neurosurgery, and Psychiatry·M Gross
Nov 1, 1982·Journal of Neurology, Neurosurgery, and Psychiatry·A E HardingJ R Ponsford
Jan 1, 1981·European Neurology·T Papapetropoulos, C P Panayiotopoulos
Jun 1, 1965·Archives of Neurology·H TSUKAGOSHIT TSUBAKI


Mar 1, 1994·Acta Neurologica Scandinavica·W Trojaborg, C H Wulff
Jul 1, 1997·Brain Pathology·M A Nance
Jan 1, 1993·Acta Neurologica Scandinavica·C Ertekin, H Sirin
Mar 1, 2004·Journal of Clinical Neuromuscular Disease·Cavit BozAhmet Karagüzel

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